Table 2.
Salford Mucopolysaccharidosis Airway Score (SMAS).
S. No. | Parameter | Measure | Score | Final Score |
---|---|---|---|---|
MPS Type | ||||
1 | Mouth opening | >5 cm | 0 | |
4–5 cm | 1 | |||
3–4 cm | 2 | |||
<3 cm | 3 | |||
2 | Teeth protrusion on clinical exam and scans | Non-protruding | 0 | |
Mild | 1 | |||
Moderate | 2 | |||
Severe | 3 | |||
3 | Cervical spine mobility, stability | unrestricted | 0 | |
60–90 degrees flexion | 1 | |||
30–60 degrees flexion | 2 | |||
<30 degrees or unstable | 3 | |||
4 | Tongue bulkiness on examination and Scan | Normal | 0 | |
Mild (filling less than 1/3 of floor mouth) |
1 | |||
Moderate (filling 1/3 to 1/2 of oral cavity) |
2 | |||
Severe (filling more than 1/2 of oral cavity) |
3 | |||
5 | Modified Mallampati grade [11] | 1 | 0 | |
2 | 1 | |||
3 | 2 | |||
4 | 3 | |||
6 | Thyromental distance | >6 cm | 0 | |
5–6 cm | 1 | |||
4–5 cm | 2 | |||
<4 cm | 3 | |||
7 | Larynx height epiglottis to soft palate | >4 cm | 0 | |
3–4 cm | 1 | |||
2–3 cm | 2 | |||
<2 cm | 3 | |||
8 | Epiglottis bulkiness | Normal (filling less than 1/3 of oropharynx) |
0 | |
Mild (filling 1/3 to 1/2 of oropharynx) |
1 | |||
Moderate (filling 1/2 to complete oropharynx) |
2 | |||
Severe (Filling entire oropharynx) |
3 | |||
9 | Supraglottis bulkiness | Normal (filling less than 1/3 of laryngopharynx) |
0 | |
Mild (filling 1/3 to 1/2 of laryngopharynx) |
1 | |||
Moderate (filling ½ to complete laryngopharynx) |
2 | |||
Severe (filling entire oropharynx) |
3 | |||
10 | Glottis bulkiness | Normal (filling less than 1/3 of glottis) |
0 | |
Mild (filling 1/3 to 1/2 of glottis) |
1 | |||
Moderate (filling 1/2 to complete glottis) |
2 | |||
Severe (filling entire glottis) |
3 | |||
11 | Subglottis diameter at cricoid level | >7 mm | 0 | |
6–7 mm | 1 | |||
5–6 mm | 2 | |||
<5 mm | 3 | |||
12 | Tracheomalacia or tracheal stenosis (degree of narrowing) |
No narrowing | 0 | |
50–75% lumen narrowing | 1 | |||
75–99% lumen narrowing | 2 | |||
100% lumen narrowing | 3 | |||
13 | Tracheal tortuosity | None | 0 | |
present | 3 | |||
14 | FEV1% | >80% | 0 | |
60–79% | 1 | |||
40–59% | 2 | |||
<40% | 3 | |||
15 | FVC% | >80% | 0 | |
60–79% | 1 | |||
40–59% | 2 | |||
<40% | 3 |