Table 1.
Clinical parameters, Brother A.
| Brother A, age 23, delF508/delF508, all tests performed June–August 2020 | |
|---|---|
| Height, Height percentile for men | 6′0”, 84th percentile |
| Weight, Weight percentile for men | 218 lbs., 72nd percentile |
| BMI | 29.6 (overweight) |
| Blood pressure | 146/84 |
| FVC (percent predicted) | 6.95 L (124%) |
| FEV1 (percent predicted) | 5.21 L (108%) |
| FEV1/FVC (percent predicted) | 74.96% |
| PEF (percent predicted) | 14.67 L/second (about 160%) |
| %SpO2 | 97% |
| CF Lower Respiratory Culture (LabCorp version) | Light Growth, Staphylococcus aureus (methicillin sensitive) |
| Hemoglobin A1c | 5.2% (Normal; normal range 4.8–5.6) |
| C-Reactive Protein | <1 mg/L (Normal; normal range 0–10) |
| Vitamin D, 25-Hydroxy | 39.1 ng/mL (Normal; normal range 39–100) |
| Beta Carotene | 6 μg/dL (Normal; normal range 3–91) |
| Vitamin A | 68.8 μg/dL (High; normal range 18.9–57.3) |
| Vitamin E (Alpha Tocopherol) | 27.6 mg/L (High; normal range 5.9–19.4) |
| Vitamin E (Gamma Tocopherol) | 0.6 mg/L (Low; normal range 0.7–4.9) |
| Total Protein | 7.5 g/dL (Normal; normal range 6.0–8.5) |
| Albumin | 4.9 g/dL (Normal; normal range 4.1–5.2) |
| Bilirubin, Total | 0.5 mg/dL (Normal; normal range 0–1.2) |
| Bilirubin, Direct | 0.13 mg/dL (Normal; normal range 0–0.40) |
| Alkaline Phosphatase | 100 IU/L (Normal; normal range 39–117) |
| AST (SGOT) | 24 IU/L (Normal; normal range 0–40) |
| ALT (SGPT) | 47 IU/L (High; normal range 0–44) |