Table 2.
Clinical parameters, Brother B.
| Brother B, age 21, delF508/delF508, all tests performed June–August 2020 | |
|---|---|
| Height, Height percentile for men | 5′ 10 ½”, 67th percentile |
| Weight, Weight percentile for men | 157.8 lbs, 19th percentile |
| BMI | 22.3 (normal) |
| Blood pressure | 122/70 |
| FVC (percent predicted) | 4.81 L (133%) |
| FEV1 (percent predicted) | 3.13 L (101%) |
| FEV1/FVC (percent predicted) | 65.07% |
| PEF (percent predicted) | 6.75 L/second (93%) |
| %SpO2 | 92% |
| CF Lower Respiratory Culture (LabCorp version) | Light Growth, Staphylococcus aureus (methicillin sensitive) |
| Hemoglobin A1c | 5.3% (Normal; normal range 4.8–5.6) |
| C-Reactive Protein | <1 mg/L (Normal; normal range 0–10) |
| Vitamin D, 25-Hydroxy | 34.9 ng/mL (Normal; normal range 0–100) |
| Beta Carotene | 6 μg/dL (Normal; normal range 3–91) |
| Vitamin A | 53.2 μg/dL (Normal; normal range 18.9–57.3) |
| Vitamin E (Alpha Tocopherol) | 15.4 mg/L (Normal; normal range 5.9–19.4) |
| Vitamin E (Gamma Tocopherol) | 0.3 mg/L (Low; normal range 0.7–4.9) |
| Total Protein | 7.2 g/dL (Normal; normal range 6.0–8.5) |
| Albumin | 4.7 g/dL (Normal; normal range 4.1–5.2) |
| Bilirubin, Total | 1.0 mg/dL (Normal; normal range 0–1.2) |
| Bilirubin, Direct | 0.25 mg/dL (Normal; normal range 0–0.4) |
| Alkaline Phosphatase | 88 IU/L (Normal; normal range 39–117) |
| AST (SGOT) | 24 IU/L (Normal; normal range 0–40) |
| ALT (SGPT) | 25 IU/L (Normal; normal range 0–44) |