Table 3.
Clinical parameters, Brother C.
Brother C, age 18, delF508/delF508, all tests performed June–August 2020 | |
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Height, Height percentile for men | 5′ 11 ½ ”, 78th percentile |
Weight, Weight percentile for men | 153.6 lbs., 15th percentile |
BMI | 21.1 (normal) |
Blood pressure | 121/71 |
FVC (percent predicted) | 6.44 L (127%) |
FEV1 (percent predicted) | 5.07 L (116%) |
FEV1/FVC (percent predicted) | 78.73% |
PEF (percent predicted) | 13.93 L/second (155%) |
%SpO2 | 97% |
CF Lower Respiratory Culture (LabCorp version) | Moderate Growth, Staphylococcus aureus (methicillin sensitive) |
Hemoglobin A1c | 5.4% (Normal; normal range 4.8–5.6) |
C-Reactive Protein | 2 mg/L (Normal; normal range 0–10) |
Vitamin D, 25-Hydroxy | 27.9 ng/mL (Low; normal range 30–100) |
Beta Carotene | 6 μg/dL (Normal; normal range 3–91) |
Vitamin A | 48.4 μg/dL (Normal; normal range 18.8–54.9) |
Vitamin E (Alpha Tocopherol) | 13.8 mg/L (High; normal range 5.0–13.2) |
Vitamin E (Gamma Tocopherol) | 0.7 mg/L (Low; normal range 0.8–3.8) |
Total Protein | 7.2 g/dL (Normal; normal range 6.0–8.5) |
Albumin | 4.6 g/dL (Normal; normal range 4.1–5.2) |
Bilirubin, Total | 0.3 mg/dL (Normal; normal range 0–1.2) |
Bilirubin, Direct | 0.10 mg/dL (Normal; normal range 0–0.4) |
Alkaline Phosphatase | 127 IU/L (Normal; normal range 56–127) |
AST (SGOT) | 27 IU/L (Normal; normal range 0–40) |
ALT (SGPT) | 36 IU/L (Normal; normal range 0–44) |