| aARS | aminoacyl-tRNA synthetases |
| ATP6 | ATP synthase membrane subunit 6 |
| ATP8 | ATP synthase membrane subunit 8 |
| CO1 | cytochrome c oxidase subunit 1 |
| CO2 | cytochrome c oxidase subunit 2 |
| CO3 | cytochrome c oxidase subunit 3 |
| CSBII | G-rich sequence block II |
| CYB | cytochrome b |
| ELAC2 | zinc phosphodiesterase ELAC protein 2 |
| FASTK | Fas-activated serine/threonine kinase |
| G4 | G-quadruplex |
| GRSF1 | G-rich sequence factor 1 |
| HSD17B10 | hydroxysteroid 17-b dehydrogenase 10 |
| HSP | H-strand promoter |
| LRPPRC | leucine-rich pentatricopeptide repeat-containing protein |
| LSP | L-strand promoter |
| MRG | mitochondrial RNA granules |
| MRPL12 | mitochondrial ribosomal protein L7/L12 |
| MRPs | mitoribosomal proteins |
| MTERF1 | mitochondrial transcription termination factor 1 |
| mt-LSU | mitochondrial ribosome large subunit |
| MTPAP | mitochondrial poly(A) polymerase |
| MTRES1 | mitochondrial transcription rescue factor 1 |
| MTS | mitochondrial targeting sequence |
| mtSSB (SSBP1) | single-stranded DNA-binding protein |
| mt-SSU | mitochondrial ribosome small subunit |
| NCR | non-coding regulatory region |
| ND1 | NADH-ubiquinone oxidoreductase chain 1 |
| ND2 | NADH-ubiquinone oxidoreductase chain 2 |
| ND3 | NADH-ubiquinone oxidoreductase chain 3 |
| ND4 | NADH-ubiquinone oxidoreductase chain 4 |
| ND4L | NADH-ubiquinone oxidoreductase chain 4L |
| ND5 | NADH-ubiquinone oxidoreductase chain 5 |
| ND6 | NADH-ubiquinone oxidoreductase chain 6 |
| OXPHOS | oxidative phosphorylation system |
| PDE12 | 3′ exonuclease phosphodiesterase 12 |
| PNPase (PNPT1) | polynucleotide phosphorylase |
| POLG | polymerase γ |
| POLRMT | mitochondrial RNA polymerase |
| PPR | pentatricopeptide repeat |
| PRORP | protein-only RNase P catalytic subunit |
| RAP | RNA-binding domain abundant in apicomplexans |
| RBP | RNA-binding protein |
| REXO2 | RNA exonuclease 2 |
| RNase P | endoribonuclease P |
| RRM | RNA recognition motif |
| SIRT1 | protein deacetylase sirtuin-1 |
| SLIRP | stem-loop-interacting RNA-binding protein |
| SUV3 (SUPV3L1) | ATP-dependent RNA helicase SUPV3L1 |
| TEFM | mitochondrial transcription elongation factor |
| TFAM | mitochondrial transcription factor A |
| TFB2M | mitochondrial transcription factor B2 |
| TRMT10C | tRNA methyltransferase 10C |