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Typical and Atypical Symptoms of SLONM in the Present Case.
| Systems | Typical | Untypical |
|---|---|---|
| Skeletal | Scoliosis | |
| Muscle | Atrophy | |
| Gowers' sign (+) | ||
| Respiratory | Type II respiratory failure | |
| Cardiovascular | Complete AV block | |
| Cardiac arrest | ||
| Right ventricular failure | ||
| Pulmonary hypertension | ||
| Orthostatic hypotension | ||
| Reflex | Hyperreflexia | |
| Trömner (+) | ||
| Babinski (+) |
AV: atrioventricular, SLONM: sporadic late-onset nemaline myopathy
