| The International Classification of Headache Disorders (ICHD) criteria for THS include the following:7 | |
| A. | Unilateral headache fulfilling criterion C |
| B. | Both of the following: |
| 1. granulomatous inflammation of the cavernous sinus, superior orbital fissure or orbit, demonstrated by MRI or biopsy | |
| 2. paresis of one or more of the ipsilateral IIIrd, IVth, and/or VIth cranial nerves | |
| C. | Evidence of causation demonstrated by both of the following: |
| 1. headache has preceded paresis of the IIIrd, IVth, and/or VIth nerves by ≤2 weeks, or developed with it | |
| 2. headache is localized around the ipsilateral brow and eye | |
| D. | Not better accounted for by another ICHD-3 diagnosis. |