Figure 5.
Remarkable translational alterations in TDPΔCR mice and HEK293ΔCR cells. (A) Representative EM micrographs and quantification showing changed ribosomal densities in hippocampal neurons of WT and TDPΔCR+/− mice (n = 18–20 neurons from 3 mice per group). (B) Schematic diagram of in vivo labeling of newly synthesized polypeptides by SUnSET in WT and TDPΔCR+/− mice. Lower panel: Representative images of newly synthesized polypeptide labeled by puromycin in the brains of WT mice. Lv, lateral ventricle; III, third ventricle; IV, fourth ventricle. (C) Representative immunoblot and quantification of newly synthesized polypeptide labeled by puromycin in the hippocampal tissues from WT and TDPΔCR+/− mice (n = 4 mice per group). (D) Representative EM micrographs and quantification showing changed ribosomal densities in WT and TDP-43ΔCR HEK293 cells (n = 11–12 cells per group). (E) Representative immunoblot and quantification of newly synthesized proteins labeled by Click-iT AHA in WT and TDP-43ΔCR HEK293 cells (n = 3 independent experiments per group). (F) Representative immunoblot and quantification of EGFP expression driven by cap-dependent (CMV-EGFP) and cap-independent (IRES-EGFP) translation in WT and TDP-43ΔCR cells (n = 3 independent experiments per group). Data are mean ± SEM; two-tailed Student’s t test. *, P < 0.05; **, P < 0.01; and ****, P < 0.0001.