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. 2021 Jul 29;13(7):e16723. doi: 10.7759/cureus.16723

Table 1. Literature review summary.

CF=Cystic fibrosis, LVEF=Left ventricular ejection fraction, LVF=Left ventricular function

No. Author/year Study Type Number of Patients with CF Results
RightVentricle Left Ventricle Blood vessel
1 Eising, J. B., et al. 2018 [15] Case-Control 33 (Children) Right ventricular dysfunction Left ventricular dysfunction Arterial stiffness
2 Sellers, Z. M., et al., 2015  [19] Prospective Cohort 8 (Age >=18 years) Normal right ventricular function Left ventricular systolic & diastolic dysfunction  
3 Zebrak, J., et al. 2000 [20] Case Series n=18 (Children)               Myocardial fibrosis and necrosis
4 Labombarda, F., et al., 2011 [23] Prospective Cohort 42 (Age >=16)   Subclinical changes in LVF  
5 Koelling, T. M., et al., 2002 [24] Case-Control 40 Right ventricular dysfunction Left ventricular diastolic dysfunction  
6 Giacchi, V., et al., 2015 [25] Case-Control 25 (Children & Adolescents), 30 (Adults) Right ventricular systolic dysfunction Decreased LVEF in adult patients  
7 Sciatti, E., et al. 2019 [33] Case-Control 22 Right ventricular subclinical systolic-diastolic dysfunction No left ventricular dysfunction  
8 Bano-Rodrigo, A., et al., 2012 [34] Case-Control 37 (Adolescents) abnormalities in right ventricular anatomy, systolic & diastolic function    
9 Ozcelic, N., et al., 2013  [35] Case-Control 18 (Children/Adolescents) Right ventricular dysfunction    
10 Florea, V., et al., 2000 [39] Case-Control 103 (Adults) Right ventricular systolic & diastolic impairment No left ventricular anomalies  
11 Vizzardi, E., et al., 2019 [40] Case-Control 22 (Adults)     Endothelial dysfunction
12 Poore, S., et al., 2013 [45] Prospective Cohort 15 (Adults)     Endothelial dysfunction