Table 1. Literature review summary.
CF=Cystic fibrosis, LVEF=Left ventricular ejection fraction, LVF=Left ventricular function
No. | Author/year | Study Type | Number of Patients with CF | Results | ||
RightVentricle | Left Ventricle | Blood vessel | ||||
1 | Eising, J. B., et al. 2018 [15] | Case-Control | 33 (Children) | Right ventricular dysfunction | Left ventricular dysfunction | Arterial stiffness |
2 | Sellers, Z. M., et al., 2015 [19] | Prospective Cohort | 8 (Age >=18 years) | Normal right ventricular function | Left ventricular systolic & diastolic dysfunction | |
3 | Zebrak, J., et al. 2000 [20] | Case Series | n=18 (Children) | Myocardial fibrosis and necrosis | ||
4 | Labombarda, F., et al., 2011 [23] | Prospective Cohort | 42 (Age >=16) | Subclinical changes in LVF | ||
5 | Koelling, T. M., et al., 2002 [24] | Case-Control | 40 | Right ventricular dysfunction | Left ventricular diastolic dysfunction | |
6 | Giacchi, V., et al., 2015 [25] | Case-Control | 25 (Children & Adolescents), 30 (Adults) | Right ventricular systolic dysfunction | Decreased LVEF in adult patients | |
7 | Sciatti, E., et al. 2019 [33] | Case-Control | 22 | Right ventricular subclinical systolic-diastolic dysfunction | No left ventricular dysfunction | |
8 | Bano-Rodrigo, A., et al., 2012 [34] | Case-Control | 37 (Adolescents) | abnormalities in right ventricular anatomy, systolic & diastolic function | ||
9 | Ozcelic, N., et al., 2013 [35] | Case-Control | 18 (Children/Adolescents) | Right ventricular dysfunction | ||
10 | Florea, V., et al., 2000 [39] | Case-Control | 103 (Adults) | Right ventricular systolic & diastolic impairment | No left ventricular anomalies | |
11 | Vizzardi, E., et al., 2019 [40] | Case-Control | 22 (Adults) | Endothelial dysfunction | ||
12 | Poore, S., et al., 2013 [45] | Prospective Cohort | 15 (Adults) | Endothelial dysfunction |