Table 3. Showing comparison of our study with previously reported studies in childhood ataxia with central nervous system hypomyelination.
Parameter | Gungor et al ( n = 11) Turkey |
Turon-Vinas et al ( n = 21) Spain |
Current study ( n = 18) India |
---|---|---|---|
Mean age of onset (mo) | NR | NR | 37 |
Infantile onset | 34 | NR | 33 |
Early childhood onset | 64 | 86 | 50 |
Late childhood onset | NR | 14 | 17 |
Consanguinity | 27 | 10 | 94 |
Epilepsy | 18 | 42 | 83 |
Course | |||
Rapidly progressive | 24 | 36 | 39 |
waxing and waning | NR | NR | 39 |
Slowly progressive | 76 | 64 | 22 |
Optic atrophy | NR | 4 (19) | 9 (50) |
Abbreviation: NR, not reported.