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. 2021 Sep 14;16:387. doi: 10.1186/s13023-021-01991-2

Table 2.

Mean cysteamine levels

Time in minutes Mean Cysteamine level (Cystagon®) Mean Cysteamine level (Procysbi®) p-value
0 3.49 ± 1.8 4.04 ± 2.88 0.96
30 34.23 ± 47.22 3.72 ± 2.78 0.001
60 56.95 ± 40.21 12.39 ± 13.16 0.002
90 56.33 ± 30.8 24.81 ± 24.24 0.002
120 47.01 ± 26.53 37.98 ± 30.09 0.43
180 23.5 ± 16.44 50.03 ± 28.46 0.002
240 11.4 ± 6.79 28.9 ± 15.87 0.001
300 8.63 ± 4.38 18.33 ± 12.19 0.003
360 6.53 ± 3.62 11.52 ± 7.08 0.016
540 5.77 ± 3.26
720 3.61 ± 2.23

This table demonstrates mean cysteamine levels in µmol/l under a single dose of IR-cysteamine (Cystagon®) and DR-cysteamine (Procysbi®) at different point of times, including standard deviations and p-values