Table 2.
Clinical and demographic data of pregnant women with pemphigus.
Authorsa | Number of women | Diagnosis before pregnancy | Diagnosis during pregnancy | Disease | Age at onset (years) | Week of gestation at the onset or worsening | Worsening during pregnancy | Improvement during pregnancy | Stable during pregnancy | Worsening in postpartum | Newborn with bullous lesions | Treatment |
---|---|---|---|---|---|---|---|---|---|---|---|---|
Lake et al. | 1 | X | PV | 24 | NA | X | C/MPM/AZA/IVIG/RTX | |||||
1 | X | PV | 19 | NA | X | C/MPM/IVIG/RTX | ||||||
Rangel | 1 | X | PV | 24 | 11 | X | X | C/RTX | ||||
Elmuradi et al. | 1 | X | PV | 33 | 24 | X | C/MPM/IVIG/RTX | |||||
Çayirli et al. | 1 | X | PV | NA | 18 | X | C/AZA | |||||
Salzberg et al. | 1 | X | PV | 34 | 6 | X | C | |||||
Kodagali et al. | 1 | X | PV | NA | NA | X | C | |||||
Solís-Arias et al. | 1 | X | PV | 21 | 3 | X | X | C | ||||
Itsukaichi et al. | 1 | X | PV | 34 | NA | X | X | X | ||||
Ibrahim et al. | 1 | X | PV | 23 | 22 | X | X | C/IVIG | ||||
Lorente Lavirgen et al. | 1 | X | PF | 33 | 24 | X | X | C | ||||
Drenovska et al. | 1 | X | PV | 27 | NA | X | X | C | ||||
1 | X | PV | 24 | X | C | |||||||
Galarza et al. | 1 | X | PF | 36 | 17 | C | ||||||
Gushi et al. | 1 | X | PV | 32 | NA | X | X | C | ||||
Lehman et al. | 1 | X | PV | 32 | NA | X | ||||||
Amer et al. | 1 | X | PV | NA | NA | X | C | |||||
Ugajin et al. | 1 | X | PV | 30 | NA | X | X | C | ||||
Bonifazi et al. | 1 | X | PV | NA | NA | PV onset 6 months post- partum | X | |||||
Fenniche et al. | 1 | X | PV | 29 | 12 | X | X | C | ||||
López-Jornet et al. | 1 | X | PV | 32 | 20 | X | C | |||||
Shieh et al. | 1 | X | PV | 29 | 16 | X | X | C | ||||
Okubo et al. | 1 | X | PV | 24 | 18 | X | X | C | ||||
Hirsch et al. | 1 | X | PF | 23 | NA | X | ||||||
Parlowsky et al. | 1 | X | PV | NA | NA | X | X | |||||
Campo-Voegeli et al. | 1 | X | PV | 35 | 8 | X | X | C | ||||
Kalayciyan et al. | 1 | X | PV | 31 | 32 | C/AZA | ||||||
1 | X | PV | 33 | 8 | C | |||||||
1 | X | PV | 32 | 10 | C | |||||||
1 | X | PV | 30 | 4 | C | |||||||
Muhammad et al. | 1 | X | PV | 28 | 8 | X | C | |||||
Masson et al. | 1 | X | PV | 38 | 12 | X | C | |||||
Avalos-Díaz et al. | 1 | X | PF | 20 | NA | X | X | C | ||||
Piontek et al. | 1 | X | PV | 29 | 12 | X | C | |||||
Fainaru et al. | 1 | X | PV | 32 | 13 | X | C | |||||
Kanwar et al. | 1 | X | PV | 33 | 24 | X | X | C | ||||
Hern et al. | 1 | X | PV | 32 | 14 | X | C | |||||
1 | X | PV | 33 | 14 | X | Symptomatic treatment | ||||||
Chowdhury et al. | 1 | X | PV | 31 | 18 | X | X | C | ||||
Virgili et al. | 1 | X | PV | 27 | 26 | X | C | |||||
Tope et al. | 1 | X | PV | 27 | NA | X | X | C | ||||
Goldberg et al. | 1 | X | PV | 21 | 28 | X | C | |||||
Kanwar et al. | 1 | X | PV | 21 | 6 | X | C | |||||
Moncada et al. | 1 | X | PV | 28 | 16 | X | X | C | ||||
Kaufman et al. | 1 | X | PF | 27 | 16 | X | C | |||||
Eyre et al. | 1 | X | PF | 37 | NA | X | C | |||||
Hup et al. | 1 | X | PV | 20 | NA | X | ||||||
Merlob et al. | 1 | X | PV | 24 | NA | X | X | C | ||||
Ross et al. | 1 | X | PV | 19 | 13 | X | Fetal death | C/AZA | ||||
Wasserstrum et al. | 1 | X | PV | 30 | 20 | X | Fetal death | C/AZA | ||||
Green et al. | 1 | X | PV | 36 | 28 | X | Fetal death | C | ||||
Moncada et al. | 1 | X | PV | 18 | 14 | X | C | |||||
Honeyman et al. | 1 | X | PV | 25 | 32 | X | C | |||||
X | PV | 29 | NA | NA | X (post- miscarriage) | Miscarriage | ||||||
X | PV | 33 | 16 | X | C | |||||||
Terpstra et al. | 1 | X | PV | 23 | 12 | X | Fetal death | C/DAPSONE | ||||
Stanoeva et al. | 1 | X | PV | 33 | 13 | X | C | |||||
1 | X | PV | 28 | 20 | X | X | C | |||||
1 | X | PV | 29 | 20 | X | C |