Table 1.
Demographics and clinical characteristics.
| DS/MMS (n = 52) | MMD (n = 77) | DS (n = 1,217) | p-value | 95% CI | |
|---|---|---|---|---|---|
| Sex ( n , %) | |||||
| Male Female |
23 (44.2) 29 (55.8) |
32 (41.6) 45 (58.4) |
578 (47.5) 638 (52.5) |
0.554 | 0.87–1.16 |
| Race/Ethnicity | |||||
| Caucasian Hispanic Asian Black Other |
85 (72,93) 37 (24,51) 10 (3,21) 4 (0, 13) 2 (0, 10) |
73 (61, 82) 40 (29,52) 21 (12, 32) 5 (1, 13) 1 (0, 7) |
87 (85,89) 35 (33,38) 9 (8,11) 4 (3,5) 0 (0, 1) |
0.011 | 0.88–1.19 |
| Age (median, IQR) | 13 (8.25–17) | 12 (6–15) | 11 (7–15) | 0.074 | 0.96–1.02 |
| History of Hypothyroidism (%, 95% CI) | |||||
| Yes No Unknown |
50 (36, 64) 50 (36, 64) 0 |
8 (3, 16) 79 (68, 88) 13 (6, 23) |
15 (13, 17) 43 (40, 45) 43 (40, 46) |
<0.001 | |
| Moyamoya Clinical Data | |||||
| % (95% CI) | % (95% CI) | p -value | |||
| Clinical presentation | |||||
| CVA TIA Headache Seizure Weakness Incidental |
71 (57, 83) 8 (2, 19) 4 (0, 13) 10 (3, 21) 8 (2, 19) 0 |
68 (56, 78) 12 (5, 21) 10 (5, 19) 9 (4, 18) 0 1 (0, 7) |
0.111 | ||
|
Preceding trigger URI/Viral syndrome Trauma Other |
23 (13, 37) 19 (10, 33) 0 4 (0, 13) |
23 (14, 34) 22 (13, 33) 1 (0, 7) 1 (0, 7) |
0.254 | ||
| Collaterals Present | 79 (65, 89) | 81 (70, 89) | 0.826 | ||
| Laterality | |||||
| Bilateral Unilateral Left Right |
73 (59, 84) 27 (16, 41) 17 (8, 30) 10 (3, 21) |
79 (68, 88) 21 (12, 32) 13 (6, 23) 8 (3, 16) |
0.775 | ||
| Suzuki grade (median, IQR) | 3 (2.25–4) | 3 (3–4) | 0.360 | ||
| Hemorrhage (n, %) | 0 | 3 (3.9) | 0.273 | ||
| Aneurysm (n, %) | 1 (1.9) | 0 | 0.403 | ||
| Posterior circulation involvement (n, %) | 14 (26.9) | 11 (19.5) | 0.391 | ||
CVA, cerebrovascular accident; IQR, interquartile range; OSA, obstructive sleep apnea; TIA, transient ischemic attack; URI, upper respiratory tract infection.