| PrPC | Endogenous prion protein |
| PrPSc | Pathogenic prion protein |
| PRNP | Prion protein gene |
| PRND | Prion-like protein gene |
| PRNT | Prion-related protein gene |
| SPRN | Shadow of prion protein gene |
| LD | Linkage disequilibrium |
| GPI | Glycosylphosphatidylinositol |
| vCJD | Variant Creutzfeldt-Jakob disease |
| UTR | Untranslated region |
| BSE | Bovine spongiform encephalopathy |
| SNPs | Single nucleotide polymorphisms |
| ORF | Open reading frame |