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. Author manuscript; available in PMC: 2021 Sep 27.
Published in final edited form as: Haemophilia. 2020 Apr 19;26(3):431–442. doi: 10.1111/hae.13960

Table 3.

Summary of studies.

Study/Year Country HA/HB Ped/Adult§ MHD assessment tool MHD prevalence n/total (%) Comorbidities n/total (%)††

Spencer 1968 US NR P/A Psychiatric evaluation Depression 3/26 (12%)
Anxiety 0/26 (0%)
NR
Klein 1982 US NR Ped BDI Depression 3/11 (27%) NR
Dew 1990 US NR A SCL90 Depression 32/75 (44%)
Anxiety 25/75 (33%)
HIV 31/75 (41%)
Burton 1991 US AB Ped CDI Depression 12/22 (55%)
Anxiety 9/22 (41%)
HIV 5/27 (19%)
Catalan 1992 UK HA NR PSE / Catego Depression 2/73 (3%)
Anxiety 3/73 (4%)
HIV 37/73 (51%)
Riedel 1992 Germany HA NR PDS Depression 28/209 (13%) HIV 181/209 (87%)
Bussing 1993 US AB Ped K-SADS Anxiety 9/23 (39%) HIV 6/23 (26%)
Mayes 1996 US AB Ped Psychiatric evaluation ADHD 19/66 (29%) HIV 18/66 (27%)
Thompson 1996 UK AB Ped CAPA Depression 1/64 (2%)
Anxiety 1/64 (2%)
ADHD 1/64 (2%)
HIV 31/64 (48%)
Miners 1999 UK AB A EQ-5D Anxiety/Depression 54/166 (33%) HIV 31/168 (18%)
Celiker 2000 Turkey AB Ped CDI Depression 2/12 (17%) Arthritis 12/12 (100%)
Shapiro 2001 US HA Ped Self-report ADHD 13/131 (10%) NR
Sadowski 2003 Int. HA Ped K-SADS Depression 7/58 (12%)
Anxiety 7/58 (12%)
ADHD 3/58 (5%)
HIV 7/58 (12%)
Arthritis 23/58 (40%)
Woodrich 2003 US AB Ped ADHD-IV scale ADHD 11/34 (32%) NR
Bahls 2006 Brazil NR Ped CDI Depression 7/20 (35%) NR
Ghanizadeh 2009 Iran AB Ped K-SADS Depression 5/83 (6%)
Anxiety 4/83 (5%)
HCV 15/83 (18%)
HBV 1/83 (1%)
Siboni 2009 Italy AB A GDS-30 Depression 18/39 (46%) HIV 5/39 (13%)
HCV 36/38 (95%)
HBV 4/38 (11%)
Arthritis 37/39 (95%)
Spencer 2009 US AB Ped ADHD-IV scale ADHD 5/18 (28%) NR
Hasan 2011 Egypt HA Ped BDI Depression 34/50 (68%) NR
Khleif 2011 US AB A Medical record review Depression 5/63 (8%) HIV 16/63 (25%)
HCV 49/63 (78%)
HBV 4/63 (6%)
Arthritis 33/63 (52%)
Iannone 2012 US AB A PHQ-9 Depression 15/41 (37%) HIV 13/41 (32%)
HCV 23/41 (56%)
Arthritis 10/41 (24%)
Abali 2014 Turkey HA Ped SCARED Anxiety 16/42 (38%) NR
Kodra 2014 Italy AB P/A EQ-5D Anxiety/Depression 28/73 (38%) NR
Ozelo 2015 Int. A P/A EQ-5D Anxiety/Depression 46/150 (31%) HIV 14/150 (9%)
Buckner 2016 US HB A EQ-5D, PHQ-9, GAD-7 Self-report Depression 66/299 (22%)
Anxiety 70/299 (23%)
Anxiety/Depression 105/243 (43%)
HIV 27/299 (9%)
HCV 15/299 (5%)
Arthritis 144/299 (48%)
Hu 2017 China HA NR CHO-KLAT Anxiety 4/22 (18%) NR
Sun 2017 Int. AB A EQ-5D, self-report Depression 88/675 (13%)
Anxiety 97/675 (14%)
Anxiety / Depression 313/675 (46%)
HIV 121/675 (18%)
HCV 289/675 (43%)
Arthritis 325/675 (48%)
Kempton 2018 US AB A EQ-5D, self-report Depression 73/381 (19%)
Anxiety 53/381 (14%)
Anxiety/Depression 165/381 (43%)
Arthritis 246/381 (65%)

Int.- international, UK- United Kingdom, US- United States

HA- haemophilia A, HB- haemophilia B, AB - haemophilia A and B

§

A- Adults, Ped- Pediatries, P/A- Pediatries and Adults

MHD- mental health disorder, BDI- Beck Depression Inventory, CAPA- Child and Adolescent Psychiatric Assessment, CDI- Children’s Depression Inventory, CHO-KLAT- Canadian Hemophilia Outcomes- Kids’ Life Assessment Tool, EQ-5D- EuroQoL five dimension scale, GAD-7- General Anxiety Disorder 7, GDS-30- Geriatric Depression Scale 30, K-SADS- Schedule for Affective Disorders and Schizophrenia for School-Aged Children, PDS- Paranoid-Depression Scale, PHQ 9- Patient Health Questionnaire 9, PSE- Present State Examination, SCARED- Screen for Child Anxiety Related Disorders, SCL90- Symptoms Checklist 90; ADHD- attention deficit hyperactivity disorder

††

HBV- hepatitis B virus, HCV- hepatitis C virus, HIV- human immunodeficiency virus, NR- not reported.