| Size of the blood vessel involved |
Involved entities |
| Large vessel vasculitis (LVV) |
Takayasu arteritis (TAK); giant cell arteritis (GCA) |
| Medium vessel vasculitis (MVV) |
Polyarteritis nodosa (PAN); Kawasaki disease (KD) |
| Small vessel vasculitis (SVV) |
Antineutrophil cytoplasmic antibody (ANCA)–associated vasculitis (AAV); microscopic polyangiitis (MPA); granulomatosis with polyangiitis (Wegener’s) (GPA); eosinophilic granulomatosis with polyangiitis (Churg-Strauss) (EGPA); immune complex SVV; anti-glomerular basement membrane (anti-GBM) disease; cryoglobulinemic vasculitis (CV); IgA vasculitis (Henoch-Schonlein); hypocomplementemic urticarial vasculitis (anti-C1q vasculitis) |
| Variable vessel vasculitis (VVV) |
Behcet’s disease (BD); Cogan’s syndrome (CS) |
| Single-organ vasculitis (SOV) |
Cutaneous leukocytoclastic angiitis; cutaneous arteritis; primary central nervous system vasculitis; isolated aortitis; others |
| Vasculitis associated with systemic disease |
Lupus vasculitis; rheumatoid vasculitis; sarcoid vasculitis; others |
| Vasculitis associated with probable etiology |
Hepatitis C virus-associated cryoglobulinemic vasculitis; hepatitis B virus-associated vasculitis; syphilis-associated aortitis; drug-associated immune complex vasculitis; drug-associated ANCA-associated vasculitis; cancer-associated vasculitis; others |
