Table 1.
Key features of catastrophic adult-onset Still disease
| Adult-onset Still disease | |
| Yamaguchi and/or Fautrel criteria | |
| Usually new-onset disease | |
| AND ≥ 1 organ failure requiring ICU management | |
| Acute respiratory failure, caused by | |
| Lung infiltrate | |
| Pleural effusion | |
| Cardio-circulatory failure | |
| Cardio-circulatory failure, caused by | |
| Non-cardiogenic shock | |
| Myocarditis | |
| Tamponade | |
| Haematologic disorder, caused by | |
| Disseminated intravascular coagulation | |
| Haemophagocytosis | |
| Thrombotic microangiopathy | |
| AND no alternative cause | |
| No infection | |
| No drug reaction | |
| No malignancy |
ICU, intensive care unit