| AK4 | adenylate kinase 4 |
| Akt | protein kinase B |
| B2M | beta-2-microglobulin |
| BrdU | bromodeoxyuridine |
| DFO | deferoxamine |
| EPAS1 | endothelial PAS domain-containing protein 1 (HIF-2α) |
| FCCP | carbonyl cyanide 4-(trifluoromethoxy)phenylhydrazone |
| HIF | hypoxia inducible factor |
| HK2 | hexokinase 2 |
| HOX | hypoxia |
| IPAH | idiopathic pulmonary arterial hypertension |
| LDHA | lactate dehydrogenase A |
| Ki-67 | marker of proliferation Ki-67 |
| NOX | normoxia |
| OCR | oxygen consumption rate |
| OXPHOS | oxidative phosphorylation |
| PASMCs | pulmonary arterial smooth muscle cells |
| PBS | phosphate-buffered saline |
| PDHK1 | pyruvate dehydrogenase kinase 1 |
| PH | pulmonary hypertension |
| RT | room temperature |
| RT-qPCR | reverse transcription quantitative polymerase chain reaction |
| scramble | scrambled siRNA (control siRNA) |
| TCA | tricarboxylic acid |
| VSMCs | vascular smooth muscle cells |