| AAC | ADP/ATP carrier |
| APC | ATP-Mg/Pi carrier |
| adPEO | autosomal dominant progressive external ophthalmoplegia |
| AGC | aspartate-glutamate carrier |
| CIC | citrate carrier |
| DIC | dicarboxylate carrier |
| HHH | hyperornithinaemia-hyperammonaemia-homocitrullinuria |
| mtDNA | mitochondrial DNA |
| ODC | oxodicarboxylate carrier |
| ORC (ORT) | ornithine carrier |
| MCF | mitochondrial carrier family |
| MPC | mitochondrial pyruvate carrier |
| SAM | S-adenosylmethionine |
| ThPP | thiamine pyrophosphate |