Table 1:
Summary of electrophysiology, CMT Exam Score (CMTES), and CMT Neuropathy Score (CMTNS).
| ulnar CMAP | median CMAP | radial SNAP (A) | CMTES/CMTNS | ||||||
|---|---|---|---|---|---|---|---|---|---|
| Patient (age) | DL <3.2 ms |
amp ≥6 mV |
CV ≥49 m/s |
DL <4.4 ms |
amp ≥4 mV |
CV ≥49 m/s |
amp ≥15 μV |
CV ≥50 m/s |
|
| case 1 (33 y) | 2.6 | 8.9 | 55 | NR | NR | NR | NR | NR | |
| II-1 (41 y) | 3.6 | 5.0 | 43 | 4.5 | 2.2 | 50 | 3.3 | 43 | 15/19 |
A: antidromic; amp: amplitude; CMAP: compound muscle action potential; CV: conduction velocity; DL: distal latency; SNAP: sensory nerve action potential