Table 4.
De novo (n = 7) | Non-de novo(n = 13) | p-valve | |
---|---|---|---|
Age at onset (years) | 4 | 13 | 0.021* |
Gender (M:F) | 5:2 | 7:6 | 0.642 |
CMTNS (median) (range) | 12 (8–19) | 11.5 (5–18) | 0.692 |
CMTNS-G (median) (range) | 1.36 (0.86–4) | 1.24 (0.28–2.5) | 0.371 |
Median CMAP (mean ± SE) | 5.14 ± 1.33 | 6.90 ± 1.20 | 0.304 |
Median MCV (mean ± SE) | 55.63 ± 4.42 | 59.16 ± 2.10 | 0.604 |
Ulnar CMAP (mean ± SE) | 4.39 ± 2.72 | 4.37 ± 0.84 | 0.909 |
Ulnar MCV (mean ± SE) | 49.80 ± 6.30 | 56.41 ± 1.88 | 0.400 |
Median SNAP (mean ± SE) | 5.00 ± 0.50 | 4.22 ± 0.86 | 0.436 |
Median SCV (mean ± SE) | 46.30 ± 5.20 | 49.98 ± 1.44 | 0.582 |
The values have significant difference (p < 0.05). CMTNS, Charcot–Marie–Tooth disease Neuropathy Scores; CMTNS-G, Charcot–Marie–Tooth disease neuropathy scores gradient; CMAP, compound muscle action potential; SNAP, sensory nerve action potential; MCV, motor nerve conduction velocity; SCV, sensory nerve conduction velocity.