. Author manuscript; available in PMC: 2022 Sep 1.

Published in final edited form as: J Pediatr Surg. 2021 Mar 28;56(9):1513–1523. doi: 10.1016/j.jpedsurg.2021.03.046

Table 1.

Recommended Hirschsprung Disease Nomenclature.

Nomenclature	Definition
Ultrashort-segment	No clear definition and usage of this term should be abandoned
Short-Segment HD	Aganglionosis up to the sigmoid colon-descending colon junction
Long-Segment HD	Aganglionosis from sigmoid colon-descending colon junction up to the cecum (ganglion cells present in colon)
Total Colonic HD	Aganglionosis of the entire colon and <5 cm of terminal ileum
Small Intestinal HD	Aganglionosis extending beyond the terminal ileum (>5 cm)
Total Intestinal HD	<20 cm of ganglionated intestine beyond the Ligament of Treitz.
Anatomic Location of extent of aganglionosis	rectum, sigmoid colon, descending colon, transverse colon, ascending colon, cecum, ileum, jejunum