TABLE 2.

Selected laboratory values for each cohort

	No levocarnitine	Levocarnitine prophylaxis	p‐value a	Levocarnitine rescue	p‐value a
At diagnosis
AST, U/L median (range)	39 (13–901)	56 (15–708)	0.109	53 (16–188)	0.353
ALT, U/L median (range)	33 (6–840)	86 (13–1,257)	<0.001	81 (6–314)	0.005
T.bili, mg/dl median (range)	0.6 (0.1–4.4)	0.8 (0.3–11.8)	0.009	0.6 (0.2–2.8)	0.249
C.bili, mg/dl median, range)	0.4 (0.0–2.2)	0.5 (0.0–7.3)	0.335	0.2 (0.0–1.1)	0.095
Peak After PEG‐ASP
AST, U/L median (range)	63 (11–6,789)	89 (16–1,493)	0.166	181 (34–6,297)	<0.001
ALT, U/L median (range)	140 (32–2850)	258 (20–862)	0.031	431 (112–2160)	<0.001
T.bili, mg/dl median (range)	1.5 (0.3–26.7)	2.4 (0.5–20.8)	0.015	6.4 (1.2–26.3)	<0.001
C.bili, mg/dl median, range	0.7 (0.0–20.7)	1.1 (0.0–19.9)	0.049	3.3 (0.0–21.8)	0.001

^a Significance in comparison to no levocarnitine cohort.