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. 2021 Nov 3;10:51. doi: 10.1186/s40164-021-00242-1

Table 2.

Overview on clinical trials of hematological malignancies treated with DNA repair inhibitors

Target Conditions Compound Phases Participants Status NCT Number
PAPR Myelodysplastic Syndrome and Acute Myeloid Leukemia Related to PARP Inhibitors (MyeloRIB) PARP Inhibitors 178 Completed NCT04326023

Acute Lymphoblastic Leukemia

Acute Myeloid Leukemia

Veliparib (ABT-888)

Temozolomide

Phase 1 66 Active, not recruiting NCT01139970

Acute Myeloid Leukemia

Recurrent Myelodysplastic Syndrome

Olaparib Phase 2 94 Recruiting NCT03953898

Leukemia

Lymphoma

veliparib Phase 1 23 Completed NCT00387608

Chronic Lymphocytic Leukemia

T-cell-prolymphocytic Leukemia

Niraparib (MK4827) Phase 1 113 Completed NCT00749502

Acute Myeloid Leukemia

Myelodysplastic Syndrome

Chronic Lymphocytic Leukemia

Mantle Cell Lymphoma

BMN-673 (talazoparib) Phase 1 33 Completed NCT01399840
Leukemia BMN 673 Phase 1 12 Recruiting NCT03974217
Acute Myeloid Leukemia

BMN 673

Decitabine

Phase 1

Phase 2

25 Active, not recruiting NCT02878785
B-cell Malignancy, Low-grade

E7449 (dual PARP1/2 and TNKS1/2 inhibitor) alone

E7449 plus TMZ

E7449 plus carboplatin and paclitaxel

Phase 1

Phase 2

41 Completed NCT01618136

Adult Acute Megakaryoblastic Leukemia

Adult Acute Myeloid Leukemia

Chronic Myelomonocytic Leukemia

Essential Thrombocythemia

Myelodysplastic Syndrome

Philadelphia Chromosome Negative, BCR-ABL1 Positive Chronic Myelogenous Leukemia

Polycythemia Vera

Recurrent Adult Acute Lymphoblastic Leukemia

Veliparib

Topotecan-Hydrochloride

Carboplatin

Phase 1 12 Active, not recruiting NCT00588991

Acute Myeloid Leukemia

Atypical Chronic Myeloid Leukemia, BCR-ABL1 Negative|

Chronic Myelomonocytic Leukemia|

Essential Thrombocythemia|

Myelodysplastic/Myeloproliferative Neoplasm|

Myelofibrosis|

Polycythemia Vera|

Veliparib

Topotecan-Hydrochloride

Carboplatin

Phase 2 60 Suspended NCT03289910

Leukemia|

Lymphoma|

Waldenstrom Macroglobulinemia|

Veliparib

Rituximab

Bendamustine-

Hydrochloride

Phase 1

Phase 2

43 Completed NCT01326702
Mantle Cell Lymphoma

CEP-9722

Gemcitabine

Cisplatin

Phase 1 24 Completed NCT01345357
DNA-PK Chronic Lymphocytic Leukemia CC-115 Phase 1 118 Completed NCT01353625
Refractory/Recurrent Acute Myeloid Leukemia

MSC2490484A (M3814)

Mitoxantrone

Etoposide

Cytarabine

Phase 1 48 Recruiting NCT03983824
Chronic Lymphocytic Leukemia MSC2490484A (M3814) Phase 1 31 Completed NCT02316197
Lymphoma, Non-Hodgkin CC-122 (Avadomide) Phase 1 15 Active, not recruiting NCT02509039
Large B-Cell, Diffuse Lymphoma, Non-Hodgkin

CC-122

Obinutuzumab

Phase 1 75 Active, not recruiting NCT02417285
Diffuse B-Cell Lymphoma

CC-122

RCHOP

Phase 1 35 Completed NCT03283202
Leukemia, Lymphocytic, Chronic, B-Cell

CC-122

Ibrutinib

Obinutuzumab

Phase 1

Phase 2

47 Completed NCT02406742

Multiple Myeloma

Lymphoma, Large B-Cell, Diffuse

CC-122 Phase 1 271 Active, not recruiting NCT01421524
Lymphoma, Large B-Cell, Diffuse

CC-122

CC-223

Rituximab

CC-292

Phase 1 174 Active, not recruiting NCT02031419

Lymphoma, Non-Hodgkin

Lymphoma, Large B-Cell, Diffuse

Lymphoma, Follicular

CC-122

JCAR017

Durvalumab

Ibrutinib

CC-220

Relatlimab

Nivolumab

CC-99282

Phase 1

Phase 2

77 Recruiting NCT03310619
Chronic Lymphoproliferative Diseases GRN163L (Imetelstat) Phase 1 48 Completed NCT00124189
Multiple Myeloma GRN163L Phase 1 40 Completed NCT00718601
Multiple Myeloma GRN163L Phase 1 20 Completed NCT00594126

Primary Myelofibrosis

Secondary Myelofibrosis

Myeloid Malignancies

GRN163L Phase 2 81 Completed NCT01731951
Myelofibrosis (JAK-Inhibitor Treatment resistance)

GRN163L

Best Available Therapy (BAT)

Phase 3 320 Recruiting NCT04576156
Myelodysplastic Syndromes

GRN163L

Placebo

Phase 2

Phase 3

225 Recruiting NCT02598661
Multiple Myeloma

GRN163L

lenalidomide

Phase 2 13 Completed NCT01242930

Essential Thrombocythemia|

Polycythemia Vera

GRN163L Phase 2 20 Completed NCT01243073
ATR Lymphomas BAY1895344 Phase 1 241 Recruiting NCT03188965

11q-deleted Relapsed/Refractory Chronic Lymphocytic Leukaemia (CLL)|

Prolymphocytic Leukaemia (PLL)|

B Cell Lymphomas

AZD6738 (Ceralasertib) Phase 1 2 Completed NCT01955668

Leukemia|

Myelodysplastic Syndrome

CMML

AZD6738 Phase 1 52 Recruiting NCT03770429
Chronic Lymphocytic Leukemia

AZD6738

Acalabrutinib

Phase 1

Phase 2

12 Active, not recruiting NCT03328273
Cancers

AZD6738

Gemcitabine

Phase 1 55 Recruiting NCT03669601
Relapsed/refractory aggressive Non-Hodgkin's Lymphoma

AZD6738

AZD9150

Acalabrutinib

Hu5F9-G4

Rituximab

AZD5153

Phase 1 30 Completed NCT03527147