COR | Recommendations |
LOE | References |
---|---|---|---|
Hypertrophic Cardiomyopathy | |||
I | ICD implantation is indicated in patients with HCM who are survivors of SCA or have spontaneous sustained VT. | B-NR | [46,70] |
IIa | For children with HCM who have ≥1 primary risk factors, including unexplained syncope, massive left ventricular hypertrophy, nonsustained VT, or family history of early HCM-related SCD. ICD placement is reasonable after considering the potential complications of long-term ICD placement. | B-NR | [71,72] |
IIb | ICD implantation may be considered in patients with HCM without the above risk factors but with secondary risk factors for SCA such extensive LGE on cardiac MRI or systolic dysfunction. | C-LD | |
IIIHarm | ICD implantation is not indicated in patients with an identified HCM genotype in the absence of known pediatric SCA risk factors. | C-LD |