| Systemic Mastocytosis (SM): |
Satisfied major criterion + one minor criteria or at least 3 minor criteria |
| Indolent SM (ISM) |
Less than 2 B findings, no C findings |
| Bone marrow mastocytosis (provisional entity) |
Less than 2 B findings, no C findings, absence of skin lesions |
| Smoldering SM (SSM) |
More than one B findings, no C finding |
| Aggressive SM (ASM) |
At least one C finding |
| SM associated to other hematological neoplasia (SM-AHN) |
SM criteria and WHO criteria for a clonal hematological neoplasm |
| Mast cell leukemia (MCL) |
BM smear >20% MC; BM biopsy diffuse infiltration of immature MC |
