Table 1.
Characteristics | |
---|---|
Patients, n (%) | 40 (100%) |
Females, n (%) | 26 (65%) |
Age at admission (years) | 12.7 ± 2.86 |
Height (meters) | 1.55 ± 0.14 |
Height z-score | 0.10 ± 1.09 |
Weight (kg) | 45.06 ± 11.46 |
Weight z-score | −0.15 ± 0.97 |
BMI | 18.29 ± 2.12 |
BMI z-score | −0.21 ± 0.77 |
CFTR genotype | |
F508del/F508del, n (%) | 14 (35%) |
F508del/other, n (%) | 19 (47.5%) |
other/other, n (%) | 7 (17.5%) |
CF comorbidities | |
Pancreatic insufficiency, n (%) | 35 (87.5%) |
CFRD, n (%) | 7 (18%) |
ABPA, n (%) | 1 (2.5%) |
Microbiology | |
P. aeruginosa, n (%) | 23 (57.5) |
-chronic, n (%) | 12 (52) |
-intermittent, n (%) | 6 (26) |
-first time, n (%) | 5 (22) |
MSSA, n (%) | 35 (87.5) |
MRSA, n (%) | 1 (2.5) |
H. influenzae, n (%) | 5 (12.5) |
S. maltophilia, n (%) | 3 (7.5) |
B. cepacia complex, n (%) | 0 |
A. fumigatus, n (%) | 6 (15) |