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. 2021 Aug 20;10(4):753–776. doi: 10.1007/s40123-021-00383-w

Table 5.

Literature reported incidence and prevalence of keratoconus stratified into worldwide, average risk, and high-risk subcategories

Study Time period Country Incidence per 100,000 Prevalence per 100,000
Rabinowitz [184] 1998 Worldwide 50
Ferdi et al. [185] 2019 Worldwide 86
Kennedy et al. [188] 1935–1982 US 2 54.5
Ihalainen [189] 1964–1984 Finland 1.5 30
Pearson et al. [180] 1989–1999 UK 4.5
Georgiou et al. [181] 1994–2000 England 3.3
Cozma et al. [182] 1997–2001 UK 3.5
Gorskova, Serosti’anov [190] 1998 Russia 0.3
Bak-Nielsen et al. [183] 2003 Denmark 1.2 44
Grünauer-Kloevekorn, Duncker [191] 2006 Germany 50
Bak-Nielsen et al. [183] 2011 Denmark 3.8
Godefrooij et al. [192] 2011–2014 Netherlands 13
Pearson et al. [180] 1989–1999 UK 20*
Georgiou et al. [181] 1994–2000 England 25* 270
Cozma et al. [182] 1997–2001 UK 32*
Assiri et al. [193] 2001–2002 Saudi Arabia 20
Ota et al. [172] 2002 Japan 12 M|5 F 50
Jonas et al. [194] 2009 India 2300
Hwang et al. [195] 2009–2014 South Korea 5.6 37
Millodot et al. [196] 2011 Israel 2340
Ziaei et al. [197] 2012 Iran 22.3
Althomali et al. [198] 2018 Saudi Arabia 8590
Akowuah et al. [199] 2021 Africa 790

*Asian subset