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. Author manuscript; available in PMC: 2022 Nov 16.
Published in final edited form as: Circulation. 2021 Sep 30;144(20):1600–1611. doi: 10.1161/CIRCULATIONAHA.121.053521

Table 2.

Main echocardiographic measures at follow-up (median time 66 months, IQR 19–126) in the overall subset of patients with available follow-up reassessment and divided according to proband status.

total
n=68
probands
n=28 (57%)
non-probands
n=21 (43%)
p-value
Echo LVEF (%) 44±14 38±14 49±12 0.001
Echo LVEF <50 (%) 57 78 39 0.001
Echo LVEF ≦35 (%) 25 37 14 0.025
Echo LVEDD (mm) 60±10 63±9 55±10 0.008
Echo RVFAC (%) 41±9 41±10 40±8 0.710
Echo RVFAC<35 (%) 14 17 11 0.505
Echo MR (%) 64 71 55 0.277

For abbreviations see Table 1