Table 4.

Comparison of timed performance test between COL6-RD, DMD and control groups

	CONTROL	COL6-RD	DMD
Climbing 4 Stairs (sec)	1.5 ± 0.3	3.6 ± 1.4++	7.6 ± 5.7++*
10m walk/run (sec)	3.1 ± 0.4	5.9 ± 1.6++	10.6 ± 6.2++*
Supine to Stand (sec)	1.9 ± 0.5	8.4 ± 3.3++	6.4 ± 0.6++
Six min walk (m)	547.0 ± 79.2	423.3 ± 95.7+	292.0 ± 123.5++*

⁺significantly different from control at p < 0.05;

⁺⁺significantly different from controls at p < 0.01;

^*significantly different from COL6-RD at p < 0.05;

COL6-RD- Collagen VI related dystrophy, DMD- Duchenne Muscular Dystrophy.