Table 3.
Number of patients in England with PKU and/or using SLPFs under the care of an NHS hospital/centre.
| Centre | Number of PKU Paediatric Patients *** |
Number of PKU Adult Patients *** |
Number of Patients on Full/Partial Phe-Restricted Diet | Number of Non-PKU Inherited Metabolic Disorder Patients Using SLPFs |
|---|---|---|---|---|
| Birmingham Women’s and Children’s Hospital | 110 | 0 | 110 | 15 |
| Evelina London Children’s Healthcare—part of Guy’s and St Thomas’ NHS Foundation Trust | 168 | 0 | 144 | 55 |
| Guy’s and St Thomas’ NHS Foundation Trust—Adult IMD service | 0 | 195 | 145 | 10 |
| Great Ormond Street Hospital | 163 | 0 | 159 | 53 |
| University Hospitals Birmingham NHS Foundation Trust—Queen Elizabeth Hospital | 0 | 153 | 134 | 30 |
| University College London Hospitals NHS Foundation Trust | 0 | 378 | 235 | 30 |
| Bradford Teaching Hospitals NHS Foundation Trust | 58 | 0 | 58 | 21 |
| Royal Manchester Children’s Hospital | 96 | 0 | 96 | 27 |
| Bristol Royal Hospital for Children | 71 | 0 | 67 | 18 |
| North Bristol NHS Trust | 0 | 58 | 41 | 1 |
| Alder Hey Children’s NHS Foundation Trust | 54 | 0 | 54 | 17 |
| Salford Royal NHS Foundation Trust | 0 | 334 | 186 | 58 |
| Cambridge University Hospitals NHS Foundation Trust | 14 | 36 | 47—of which 14 are paediatric patients | 3 |
| Sheffield Children’s NHS Foundation Trust | 52 | 0 | 42 | 21 |
| Sheffield Teaching Hospitals NHS Foundation Trust | 0 | 160 | 90 | 20 |
| University Hospitals of Leicester NHS Trust | 13 | 0 | 10 | 12 |
| Nottingham University Hospitals NHS Trust | 24 | 0 | 24 | 9 |
| Great North Children’s Hospital—within the Royal Victoria Infirmary | 64 | 0 | 63 | 9 |
| Royal Victoria Infirmary—Adult IMD services | 0 | 74 | 43 | 5 |
| Norfolk and Norwich University Hospital | 15 | 0 | 15 | - |
| Royal Derby Hospital | 6 | 6 | 6—all of which are paediatric patients | - |
| Somerset NHS Foundation Trust | (1) | 8 (+1) | 5 (+1) | 3 |
| Royal Devon & Exeter NHS Foundation Trust | 1 (+1) | 9 | 5 (+1)—1 of which is a paediatric patient and not shared care | 2 |
| University Hospital Southampton NHS Foundation Trust | 4 (+7) | 23 (+1) | 23 (+8)—4 of which are paediatric patients and not shared care | 3 |
| Northamptonshire Healthcare NHS Foundation Trust | 10 | 2 | 12—10 of which are paediatric patients | 0 |
| University Hospitals Bristol & Weston NHS Foundation Trust | 0 | (21) | (20) | 0 |
| TOTAL | 923 | 1436 | 1814—877 of which are paediatric patients | 422 |
Abbreviations: SLPFs = special low protein foods; PKU = phenylketonuria; Phe = phenylalanine. ( ) shared care with another unit so numbers not included in totals. *** This includes patients with mild PKU/hyperphenylalaninaemia who maintain phenylalanine levels within target therapeutic range without dietary treatment.