Table 3.

A. In a patient with a clinically pure sensory neuropathy a diagnosis of sensory neuronopathy is considered as possible if score > 6.5

Ataxia in the lower or upper limbs at onset or full development	+ 3.1
Asymmetrical distribution of sensory loss at onset or full development	+ 1.7
Sensory loss not restricted to the lower limbs as full development	+ 2.0
At least 1 SAP absent or 3 SAP < 30% of the lower limit of normal in the upper limbs, not explained by entrapment neuropathy	+ 2.8
Less than two nerves with abnormal motor nerve conduction studies in the lower limbs	+ 3.1
If > 6.5, a diagnosis of SNN is possible	Total:
B. A diagnosis of sensory neuronopathy is probable if the patient’s score is > 6.5 and if
1. The initial workup does not show biological perturbations or ENMG findings excluding SNN and
2. The patient has one of the following disorders: onconeural antibodies or a cancer within 5 years (Graus et al., 2004), cisplatin treatment, Sjögren’s syndrome (Vitali et al., 2002)
3. Or MRI shows high signal in the posterior column of the spinal cord

SNN sensory neuronopathy