Table III.
Detailed characteristics of our myeloproliferative neoplasms patients with precapillary pulmonary hypertension
No. | Age, gender | Type of MPN | Disease duration | ECHO derived sPAP | ECG | NT-proBNP [pg/ml] | VEGF [pg/ml] | Type of PH | RHC | Specific treatment for PH | Survival after PH diagnosis |
---|---|---|---|---|---|---|---|---|---|---|---|
1 | 68 years, female | ET | 5 years | 90 mm Hg | Sinus rhythm RBBB |
5910 | 889 | Precapillary (Group 5) | Mean PAP: 63 mm Hg PAWP: 8 mm Hg CO: 2.2 l/min PVR: 25 Wood |
Tadalafil, macitentan | 28 months, living |
2 | 71 years, male | PV | 9 years | 71 mm Hg | Sinus rhythm RBBB |
7847 | 138 | CTEPH | Refused | Refused | 6 months, deceased |
sPAP – systolic pulmonary artery pressure, RHC – right heart catheterization, PH – pulmonary hypertension, ET – essential thrombocythemia, PV – polycythemia vera, HU – hydroxyurea, RBBB – right bundle branch block, CTEPH – chronic thromboembolic pulmonary hypertension, PAWP – pulmonary artery wedge pressure, CO – cardiac output, PVR – pulmonary vascular resistance.