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. 2020 Feb 27;17(6):1628–1635. doi: 10.5114/aoms.2020.93315

Table III.

Detailed characteristics of our myeloproliferative neoplasms patients with precapillary pulmonary hypertension

No. Age, gender Type of MPN Disease duration ECHO derived sPAP ECG NT-proBNP [pg/ml] VEGF [pg/ml] Type of PH RHC Specific treatment for PH Survival after PH diagnosis
1 68 years, female ET 5 years 90 mm Hg Sinus rhythm
RBBB
5910 889 Precapillary (Group 5) Mean PAP: 63 mm Hg
PAWP: 8 mm Hg
CO: 2.2 l/min
PVR: 25 Wood
Tadalafil, macitentan 28 months, living
2 71 years, male PV 9 years 71 mm Hg Sinus rhythm
RBBB
7847 138 CTEPH Refused Refused 6 months, deceased

sPAP – systolic pulmonary artery pressure, RHC – right heart catheterization, PH – pulmonary hypertension, ET – essential thrombocythemia, PV – polycythemia vera, HU – hydroxyurea, RBBB – right bundle branch block, CTEPH – chronic thromboembolic pulmonary hypertension, PAWP – pulmonary artery wedge pressure, CO – cardiac output, PVR – pulmonary vascular resistance.