Table 3.
Associations between DAS-II GCA and VABS-II ABC standard scores and HS-FOCUS items
| HS-FOCUS item | DAS-II GCA score coefficient (standard error) | VABS-II ABC score coefficient (standard error) |
|---|---|---|
| Activities (domain score) | −0.00714 (0.00364) | −0.01233* (0.00520) |
| Go out with friends and/or family | −0.00823* (0.00396) | −0.01214* (0.00583) |
| Take part in physical activities for 1 h | −0.00780 (0.00439) | −0.01337* (0.00614) |
| Breathing (domain score) | 0.00170 (0.00424) | 0.00689 (0.00606) |
| Do daily activities without losing breath | −0.00427 (0.00472) | 0.00692 (0.00682) |
| Sleep without snoring | 0.00635 (0.00612) | 0.01870* (0.00857) |
| Talk to someone else without losing breath | 0.00171 (0.00421) | −0.00049 (0.00623) |
| Breathe without making noise at rest | 0.00369 (0.00538) | 0.00747 (0.00781) |
| Grip/reach (domain score) | −0.00775** (0.00277) | −0.01074** (0.00411) |
| Place palm and fingers flat on a table | −0.01190 (0.00611) | −0.00676 (0.00862) |
| Throw/catch a medium-sized ball | −0.00927* (0.00390) | −0.01107 (0.00557) |
| Pour a drink into a cup | −0.00688 (0.00559) | −0.01340 (0.00788) |
| Reach all parts of his body | −0.01549* (0.00702) | −0.00972 (0.00961) |
| Button a shirt | −0.00832 (0.00672) | −0.01516 (0.00915) |
| Put on shoes while sitting in a chair | 0.00344 (0.00627) | −0.01324 (0.00923) |
| Touch the top of his head | −0.00838 (0.00530) | −0.00844 (0.00775) |
| Turn pages in a book | −0.00662* (0.00306) | −0.00616 (0.00443) |
| School/work (domain score) | −0.01221*** (0.00304) | −0.00853 (0.00452) |
| Finish all classroom assignments | −0.01551** (0.00495) | −0.00842 (0.00724) |
| Attend a full day of school or work | −0.00488 (0.00353) | −0.00522 (0.00491) |
| Walking/standing (domain score) | −0.00163 (0.00230) | −0.00230 (0.00325) |
| Walk up a flight of stairs | 0.00267 (0.00243) | 0.00151 (0.00345) |
| Stand without getting tired for 10 min | 0.00055 (0.00337) | 0.00067 (0.00489) |
| Step on a stool | −0.00695 (0.00339) | −0.00116 (0.00493) |
| Walk without getting tired for 15–20 min | 0.00468 (0.00430) | 0.00340 (0.00604) |
| Walk for 20 m (yards) without stopping | 0.00531 (0.00507) | −0.00842 (0.00722) |
Bold font indicates statistically significant associations and asterisks denote p values (*p < 0.05, **p < 0.01, ***p < 0.001). A negative association indicated that increasing cognitive function/adaptive behavior (assessed using DAS-II GCA/VABS-II ABC scores) was associated with improved functional performance (assessed using the HS-FOCUS)
ABC Adaptive Behavior Composite; DAS-II Differential Ability Scales, second edition; GCA General Conceptual Ability; HS-FOCUS Hunter Syndrome-Functional Outcomes for Clinical Understanding Scale; VABS-II Vineland Adaptive Behavior Scales, second edition