Skip to main content
. 2021 Nov 25;12:775412. doi: 10.3389/fimmu.2021.775412

Table 1.

Laminin-332 pemphigoid patients with IgG reactivity against a single subunit of laminin-332.

ID Age Sex IIF Dermal Laminin Domain reactivity Other autoantibodies
LAMA3-IgG1 85 M +40 α3
LAMA3-IgG2 61 M +10 α3
LAMA3-IgG3 63 M +10 α3 BP180/BP230
LAMA3-IgG4 50 F +10 α3
LAMB3-IgG1 NR NR +10 β3 BP180
LAMB3-IgG2 NR NR +10 β3
LAMB3-IgG3 49 F +10 β3
LAMB3-IgG4 78 M +10 β3
LAMC2-IgG1 56 F γ2
LAMC2-IgG2 74 M +10 γ2
LAMC2-IgG3 84 M +10 γ2 P200
LAMC2-IgG4 69 M +10 γ2

IIF, indirect immunofluorescence; NR, No record. IIF was performed on salt split human skin with serial dilution to 1:10 and 1:40. Laminin subunit reactivity was determined by immunoblotting. The presence of BP180, BP230, and collagen 7 antibodies was assessed by ELISA. Notably, neither patient with BP180 antibodies demonstrated epidermal staining. Immunoblotting was used to screen sera for reactivity against p200.