Table 1.

Demographics and Baseline Clinical Features of the Eight Patients

ID	Sex	Age (y)	Onset (y)	BCVAa	SE (D)	AL (mm)	Lens	Inheritance
1	M	20	AS	79 (20/25)	−1.25	24.33	Clear	AD
2	M	38	24b	84 (20/20)	+1.00	22.50	Clear	AR
3	F	55	20b	80 (20/25)	+3.00	21.84	Mild PSCC	AR
4	F	37	AS	85 (20/20)	−2.00	24.07	Clear	AR
5	F	42	34c	88 (20/20)	−8.25	27.71	Clear	Simplex
6	F	49	10c	80 (20/25)	+0.50	23.69	Clear	Simplex
7	M	22	14b	69 (20/40)	−0.50	23.80	Mild PSCC	Simplex
8	F	46	38c	84 (20/20)	+0.75	22.46	Clear	Simplex

AL, axial length; AD, autosomal dominant; AR, autosomal recessive; AS, asymptomatic; PSCC, posterior subcapsular cataract; RP, retinitis pigmentosa; SE, spherical equivalent.

^aETDRS letters at 4 m. Snellen equivalents are shown in parentheses.

^bNyctalopia.

^cVisual field constriction.