IVthV	Fourth ventricle
5AZA-DC	DNA methylase transferase inhibitor 5-aza-2′-deoxycytidine
AKT	Protein kinase B
ATRX/DAXX	Alpha-thalassemia, mental retardation, X-linked/death domain–associated protein complex
AURKA	Auro A-kinase
BET	Bromodomain and extraterminal domain
Brd4	Bromodomain-containing protein 4
c-KIT	Proto-oncogene encoding tyrosine-protein kinase KIT, CD117, or stem cell growth factor receptor
c-MYB	c-myeloblastosis
CAR T	Chimeric antigen receptor T cell
Cbp	CREB-binding protein
Cdc42	Cell division cycle 42
COX2	Cyclooxygenase-2
CNS	Central nervous system
CRL4	Cullin Ring Ubiquitin Ligase 4
CSF	Cerebrospinal fluid
CXCR4	C-X-C chemokine receptor type 4
EANO	The European Association of Neuro-Oncology
EED	Embryonic ectoderm development
EMA	Epithelial membrane antigen
Ep300	Histone acetyltransferase p300
EPHA7	Ephrin type-A receptor 7
ERK	Extracellular Signal-Regulated Kinase
ERM	Ezrin, radixin, moesin binding protein
EZHIP	EZH Inhibitory Protein or CXorf67
EZH2	Enhancer of zeste homolog 2
FAK	Focal Adhesion Kinase
FAM 118B	Family with sequence similarity 118 member B
FGFR3	Fibroblast growth factor receptor 3
FOXJ1	Forkhead box protein J1
GFAP	Glial fibrillary acidic protein
GTR	Gross total resection
H3K27M	Histone H3 lysine 27 to methionine mutation
H3K27me3	Trimethylated histone H3 at lysine 27
HDAC	Histone deacetylase
HE	Hematoxylin and eosin
HIF-1a	Hypoxia inducible factor 1 alpha
HOXA13	Homeobox A13
HOXB13	Homeobox B13
HOXC10	Homeobox C10
HOXD10	Homeobox D10
hTERT	Human telomerase reverse transcriptase
IkBα	Nuclear factor of kappa light polypeptide gene enhancer in B cells alpha
IL-6	Interleukin-6
IT	Infratentorial
KDM6	Lysine-specific demethylase 6
KIT	Tyrosine protein kinase or stem cell growth factor receptor or CD117
L1CAM	L1 Cell Adhesion Molecule
LATS1/2	Large Tumor Suppressor Kinase 1 and 2
LDOC	Leucine zipper downregulated in cancer 1
MAML2	Mastermind like transcription coactivator 2
MAMLD1	Mastermind like domain containing 1
MDM2	Mouse double minute 2 homolog or E3 ubiquitin-protein ligase Mdm2
MEF	Myocyte enhancer factor
MPE	Spinal myxopapillary ependymoma
mTORC1	Mammalian Target of Rapamycin Complex 1
MYCN	Myelocytomatosis-N
NCOA1	Nuclear receptor coactivator 1
NCOA2	Nuclear receptor coactivator 2
NEFL	Neurofilament light chain
NEC	Not elsewhere classified
NF-κB	Nuclear factor-κB
NF2	Neurofibromatosis type 2
NHERF1/EBP50	Na+/H+ exchanger regulatory factor/ezrin-radixin-moesin binding protein 50
NOS	Not otherwise specified
OS	Overall survival
PAK	P21 activated kinase
PARP	Poly (ADP-ribose) polymerase
PDGFRA	Platelet derived growth factor alpha
PFA	Posterior fossa ependymoma Group A
PFB	Posterior fossa ependymoma Group B
PFE	Posterior fossa ependymoma
PF-SE	Posterior fossa subependymoma
PFS	Progression-free survival
PI3K	Phosphoinositide 3-kinase
PIKE-L	Phosphoinositide 3-Kinase Enhancer-brain specific isoform
PLAGL	PLAG1 like zinc finger 1
PRC2	Polycomb repressive complex 2
Rac1	Ras-related C3 botulinum toxin substrate 1
RAC	Ras-related C3 botulinum toxin
RAF	Rapidly accelerated fibrosarcoma
Ras	Rat sarcoma virus
RELA	REL-associated protein
SAM	S-adenosyl methionine
SE	Subependymoma
SET	Su(var)3-9/enhancer-of-zeste/trithorax
Shh	Sonic hedgehog
SP	Spinal
SPE	Spinal ependymoma
SPE-MYCN	Spinal ependymoma with MYCN amplification
SP-SE	Spinal subependymoma
ST	Supratentorial
ST-RELA	Supratentorial ependymoma with RELA fusion
ST-SE	Supratentorial subependymoma
ST-YAP1	Supratentorial ependymoma with YAP1 fusion
STAT	Signal transducer and activator of transcription
STE	Supratentorial ependymoma
STR	Subtotal resection
SUZ12	Suppressor of zeste 12 homolog
TEAD	Transcriptional enhancer factor domain
TAZ	Gene encoding protein Tafazzin
VEGF	Vascular endothelial growth factor
WHO	World Health Organization
WP744	4′-O-benzylated doxorubicin analog
WP1066	JAK2/STAT3 inhibitor
WP1193	JAK2/STAT3 inhibitor
YAP1	Yes1 associated transcriptional regulator or YAP or YAP65
ZFTA	Zinc finger translocation-associated