Table 4.
Patients/diagnosis
|
Age at OVT (yr)
|
AST (NV ≤ 45 U/L)
|
ALT (NV ≤ 45 U/L)
|
GGT (NV ≤ 50 U/L)
|
Response to OVT 1 |
SCOPE index score2
|
Time on OVT (mo)
|
OVT side-effect
|
Overall FU3 (mo)
|
||||||||||
Before OVT
|
After OVT
|
TTN
|
Result
|
Before OVT
|
After OVT
|
TTN
|
Result
|
Before OVT
|
After OVT
|
TTN
|
Result
|
Before OVT
|
After OVT
|
||||||
AIH | 5.4 | 212 | 39 | 4 mo | NV | 147 | 17 | 6 mo | NV | 73 | 22 | 6 mo | NV | Complete | 3 low risk | 0 low risk | 99 | None | 113 |
AIH | 11.8 | 251 | 31 | 2 mo | NV | 359 | 39 | 9 mo | NV | 26 | 34 | 8 mo | NV | Complete | 3 low risk | 0 low risk | 72 | None | 73 |
ASC | 16.8 | 98 | 47 | 3 mo | < 1.5 NV | 140 | 70 | 4 | < 1.5 NV | 39 | 83 | 4 | < 1.5 NV | Partial | 8 high risk | 8 high risk | 16 | None | 26 |
ASC | 4.8 | 86 | 28 | 7 d | NV | 156 | 38 | 14 d | NV | 84 | 44 | 14 d | NV | Complete | 4 medium risk | 1 low risk | 37 | None | 39 |
ASC | 13.1 | 60 | 14 | 1 mo | NV | 365 | 38 | 3 mo | NV | 68 | 27 | 4 mo | NV | Complete | 5 medium risk | 2 low risk | 31 | None | 84 |
ASC | 15.2 | 71 | 40 | 14 mo | NV | 140 | 56 | 14 mo | < 1.5 NV | 52 | 164 | 12 mo | - | None | 6 high risk | 6 high risk | 6 | None | 68 |
ASC | 17.4 | 113 | 65 | 1 mo | < 1.5 NV | 205 | 141 | 1 mo | - | 49 | 226 | 1 mo | - | None | 6 high risk | 4 medium risk | 3 | None | 52 |
ASC | 15 | 407 | 30 | 6 mo | NV | 856 | 35 | 6 mo | NV | 61 | 28 | 1 mo | NV | Complete | 5 medium risk | 2 low risk | 40 | None | 49 |
ASC | 17.3 | 102 | 37 | 2 mo | NV | 111 | 36 | 2 mo | NV | 135 | 82 | 5 mo | < 1.5 NV | Partial | 6 high risk | 4 medium risk | 18 | None | 61 |
ASC | 12.5 | 76 | 31 | 2 mo | NV | 124 | 40 | 7 mo | NV | 86; TX | 42 | 6 mo | NV | Complete | 5 medium risk | 4 medium risk | 47 | None | 135 |
ASC | 13.9 | 123 | 155 | - | - | 165 | 154 | - | - | 165 | 1800 | - | - | None | 8 high risk | 8 high risk | 6 | None | 86; TX |
ASC | 13.2 | 141 | 135 | - | - | 156 | 180 | - | - | 71 mo (range 26-165) | 136 | - | - | None | 7 high risk | 7 high risk | 4 | None | 165 |
Response to OVT | 10/12 (83%) | 9/12 (75%) | 8/12 (67%) | Median: 34 (range 1-99) | 71 (range 26-165) |
Complete response is defined as “normalization of all three liver enzymes [aspartate aminotransferase (AST), alanine aminotransferase (ALT) and gamma-glutamyl transferase (GGT)]”, partial response as “AST, ALT or GGT levels decreasing to < 1.5 × ULN without reaching normal value”, and no response as “no significant changes in liver enzymes”.
Sclerosing Cholangitis Outcomes in Pediatrics: Points 0-3: Low risk; Points 4-5: Medium risk; Points 6-11: High risk.
Time from diagnosis to last follow up visit.
AIH: Autoimmune hepatitis; ASC: Autoimmune sclerosing cholangitis; OVT: Oral vancomycin treatment; AST: Aspartate aminotransferase; ALT: Alanine aminotransferase; GGT: Gamma-glutamyl transferase; TTN: Time to normalize or to achieve the lowest value; NV: Normal value; FU: Follow up; SCOPE: Sclerosing Cholangitis Outcomes in Pediatrics.