Table 5.
Final diagnoses.
| Final Diagnoses | n (%) | Mean (Min–Max) Diagnostic Delay, Days |
|---|---|---|
| Infections | 2/57 (4) | 20 (16–24) |
| Endocarditis with negative blood culture | 1 | |
| Acute Q fever | 1 | |
| Neoplasms | 10/57 (18) | 357 (38–1267) |
| Hematological malignancies | 8 | 418 (38–1267) |
| Hodgkin’s lymphoma | 2 | |
| Myelodysplastic syndrome * | 2 | |
| Large B-cell lymphoma ** | 1 | |
| Acute myelomonocytic leukemia | 1 | |
| Castleman’s disease | 1 | |
| Thymoma | 1 | |
| Solid tumors | 2 | 112 (69–154) |
| Uterine leiomyosarcoma | 1 | |
| Soft tissue sarcoma | 1 | |
| Noninfectious inflammatory diseases | 13/57 (23) | 67 (5–279) |
| Giant cell arteritis | 7 | 45 (7–90) |
| Microscopic polyangiitis | 3 | |
| Takayasu arteritis | 1 | |
| Adult-onset Still’s disease | 1 | |
| Sarcoidosis | 1 | |
| Miscellaneous | 1/57 | 688 |
| Sweet’s syndrome | ||
| Unknown/uncertain | 31/57 (54) |
* One associated with paraneoplastic polymyalgia rheumatic, and one with phenotype compatible with VEXAS (vacuoles, E1 enzyme, X-linked, autoinflammatory, somatic) syndrome. ** Associated with paraneoplastic polymyalgia rheumatica.