Figure 2.
Proximal myopathy and skin lesions are the clinical hallmarks in patients with jIIM. Mild facial erythema (A) and discrete erythematous papules overlying the metacarpal joints (Gottron’s papules) (B) in a 16-year-old girl with DM (P5). Coronal MR images in a 10-year-old patient with anti-NXP2 antibody-associated DM (P4) showing mild contrast enhancement in T1-weighted images and diffuse oedema of the thigh muscles at first presentation (arrows) (C) resolving completely with treatment after 6 (D) and 12 months (E).
