Table 1.

Summary of Clinicopathological characteristics and outcomes.

Clinicopathological characteristics	Case 1	Case 2	Case 3	Case 4
Age	45	27	37	25
Parity	2	2	1	0
Site at presentation	Labia Majora	Labia Majora	Labia Majora	Mons pubis, Anterior abdominal wall, Lungs
Mean size (cm)	2x2	3x2	8x8	6x6
Initial symptoms	Mass lesion	Mass lesion	Mass lesion	Mass lesion, Pain
Diagnosis at local institution	Squamous cell carcinoma	Fibroma	Malignant tumor with rhabdoid morphology	Vulval abscess
Immunohistochemical results*	Case 1 AE1/AE3+, CD34+, S100P-, P63-, P40-, CK7-. Loss of INI1/SMARCB1	Case 2 AE1/AE3+, EMA+, CD34-Focal+, CA125 + . Loss of INI1/SMARCB1	Case 3 AE1/AE3+, EMA+, Desmin-, S100P-. Loss of INI1/SMARCB1	Case 4 AE1/AE3 + . EMA + . CD34-F + . S100P-. Loss of INI1/SMARCB1
Operability at presentation	Operable	Operable	Operable	Inoperable (Distant metastasis)
Upfront treatment modality	Radical local excision	Radical local excision	Radical local excision (revision surgery)	Palliative chemotherapy
Groin node dissection	None	Ipsilateral	Bilateral	–
Adjuvant treatment	RT	RT	None	–
Follow up period (months)	72	24	12	2
Recurrence	Yes	No	No	–
Clinical outcome	Alive with disease	No evidence of disease	No evidence of disease	Alive with disease

^*"+" implies Positive staining result."- "implies negative staining result, "NA" implies stain not applied.