| RV | right ventricular |
| PAH | pulmonary arterial hypertension |
| miR-21 | microRNA-21 |
| HF | heart failure |
| AVS | Aorto-venous fistula |
| IPAH | idiopathic PAH |
| CTD | connective tissue disease |
| CHD | congenital heart disease |
| RHC | right heart catheterization |
| PCWP | pulmonary capillary wedge pressure |
| PVR | pulmonary vascular resistance |
| PAP | pulmonary arterial pressure |
| PCWP | pulmonary capillary wedge pressure |
| CO | cardiac output |
| EF | ejection fraction |
| FS | fractional shortening |