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. 2022 Jan 26;11(3):417. doi: 10.3390/cells11030417

Table 2.

Classification of SMA.

SMA Type Age of Onset Maximum Age of Survival SMN2 Copy Number Alternate Name
0 Prenatal <1 month 1 -
1 0–6 months <2 years 2 Werdnig–Hoffman disease
2 <18 months >2 years 3,4 Dubowitz disease
3a (juvenile onset) 18 months–3 years Adult 3,4 Kugelberg–Welander disease
3b >3 years Adult 4 Kugelberg–Welander disease
4 > 21 years Adult 4–8 -