Table 1.
Demographic and clinical characteristics
| All patients n = 32 (%) | Thrombosis n = 9 (%) | Non-thrombotic n = 23 (%) | P value | |
|---|---|---|---|---|
| Sex (female/male) | 21/11 | 4/5 | 17/6 | 0.11 |
| Age (years) | 11.7 (1–15) | 12.2 (1–15) | 11.5 (6–15) | 0.93 |
| Evolution time (weeks) | 16 (1–108) | 7.5 (1–28) | 19 (1–108) | 0.21 |
| Hematologic | 29 (90%) | 7 (78%) | 22 (96%) | |
| Thrombocytopenia | 22 (67%) | 7 (78%) | 15 (65%) | 0.49 |
| AIHA | 13 (41%) | 2 (22%) | 11 (48%) | 0.18 |
| LAHP | 2 (6%) | 0 | 2 (9%) | 0.36 |
| Dermatologic | 23 (72%) | 7 (78%) | 16 (70%) | |
| Livedo reticularis | 20 (63%) | 7 (78%) | 13 (57%) | 0.26 |
| Raynaud's phenomenon | 8 (25%) | 2 (22%) | 6 (26%) | 0.82 |
| Skin ulcers | 2 (6%) | 0 | 2 (9%) | 0.36 |
| Neurologic | 5 (16%) | 1 (11%) | 4 (17%) | |
| Migraine | 3 (9%) | 1 (11%) | 2 (9%) | 0.83 |
| Cognitive impairment | 3 (9%) | 1 (11%) | 2 (9%) | 0.83 |
| Epilepsy | 1 (3%) | 1 (11%) | 0 | 0.10 |
| Chorea | 1 (3%) | 0 | 1 (4%) | 0.52 |
| Renal | 4 (13%) | 3 (33%) | 1 (4%) | |
| Nephrotic síndrome | 1 (3%) | 1 (11%) | 0 | 0.10 |
| Nephritic syndrome | 3 (9%) | 2 (22%) | 1 (4%) | 0.11 |
| Clinical profile | ||||
| T | 1 (3%) | 1 (11%) | 0 | |
| H | 6 (19%) | 0 | 6 (26%) | |
| R | 1 (3%) | 1 (11%) | 0 | |
| C | 1 (3%) | 0 | 1 (4%) | |
| H + C | 16 (50%) | 5 (55%) | 11 (48%) | |
| H + N | 1 (3%) | 0 | 1 (4%) | |
| H + C + R | 2 (6%) | 1 (11%) | 1 (4%) | |
| H + C + N | 3 (9%) | 0 | 3 (13%) | |
| H + C + N + R | 1 (3%) | 1 (11%) | 0 | |
LAHP Lupus anticoagulant with hypoprothrombinemia syndrome, AIHA Autoimmune hemolytic anemia, T Thrombosis, H Hematologic, R Renal, C Cutaneous, N Neurologic