Table 2. Cancer-Associated Germline Sequence Variations in Patients With PDAC in the Nanjing Cohort.
Case ID | Chromosome position | Sex | Age, y | Gene | Amino acid change | Nucleotide change | Function | ClinVara | Personal history of other disease | Family history of cancer |
---|---|---|---|---|---|---|---|---|---|---|
P1720 | chr11:108106561 | Female | 71 | ATM | p.Glu166Gln | c.496G>C | Missense | Pathogenic | Negative | Negative |
P0251 | chr11:108153468 | Female | 65 | ATM | p.Tyr1203Ter | c.3609delT | Nonsense | Pathogenic | Negative | Negative |
P1659 | chr11:108170440 | Male | 51 | ATM | Splice | c.5006-1G>A | Noncoding | Likely pathogenic | Negative | Negative |
P2296 | chr11:108178646 | Male | 64 | ATM | p.Cys1899Ter | c.5697C>A | Nonsense | Pathogenic | Negative | Negative |
P2281 | chr11:108186639 | Female | 60 | ATM | Splice | c.6095 + 1G>A | Noncoding | Likely pathogenic | Negative | Negative |
P0537 | chr17:41197809 | Female | 66 | BRCA1 | p.Ile1845fs | c.5533_5540delATTGGGCA | Frameshift | Pathogenic | Breast cancer, lymphoma | Negative |
P2289 | chr17:41219625 | Male | 66 | BRCA1 | p.Asp1713Asn | c.5137G>A | Missense | Likely pathogenic | Negative | Negative |
P1565 | chr17:41245390 | Male | 47 | BRCA1 | p.Glu720fs | c.2157_2158insA | Frameshift | Pathogenic | Negative | Negative |
P0907 | chr13:32900280 | Male | 70 | BRCA2 | p.Lys157fs | c.470_474delAGTCA | Frameshift | Pathogenic | Negative | Negative |
P1473 | chr13:32906915 | Male | 55 | BRCA2 | p.Lys437fs | c.1310_1313delAAGA | Frameshift | Pathogenic | Negative | Negative |
P2349 | chr13:32907029 | Male | 51 | BRCA2 | p.Gln472Ter | c.1414C>T | Nonsense | Pathogenic | Negative | Negative |
P0418 | chr13:32907371 | Female | 74 | BRCA2 | p.Lys586Ter | c.1756A>T | Nonsense | Pathogenic | Lung cancer | Negative |
P1449 | chr13:32911228 | Male | 61 | BRCA2 | p.Thr915fs | c.2743_2747delACTTG | Frameshift | Pathogenic | Negative | Negative |
P0796 | chr13:32912337 | Male | 40 | BRCA2 | p.Val1283fs | c.3847_3848delGT | Frameshift | Pathogenic | Negative | Negative |
P1579 | chr13:32914102 | Female | 63 | BRCA2 | p.Lys1872fs | c.5616_5620delAGTAA | Frameshift | Pathogenic | Ovarian cancer | Negative |
P0703 | chr13:32921033 | Male | 61 | BRCA2 | p.Arg2336His | c.7007G>A | Missense | Pathogenic | Negative | Negative |
P2247 | chr13:32944538 | Male | 64 | BRCA2 | Splice | c.8332-1G>T | Noncoding | Likely pathogenic | Negative | Negative |
P2372 | chr16:23614914 | Male | 48 | PALB2 | p.Leu1143fs | c.3426_3427insA | Frameshift | Pathogenic | Negative | Negative |
P0375 | chr16:23619181 | Female | 67 | PALB2 | Splice | c.3350 + 4A>G | Noncoding | Pathogenic | Negative | Negative |
P1670 | chr16:23635403 | Male | 66 | PALB2 | p.Gln921fs | c.2760_2761insA | Frameshift | Pathogenic | Negative | Negative |
P1649 | chr16:23641218 | Male | 77 | PALB2 | p.Arg753Ter | c.2257C>T | Nonsense | Pathogenic | Negative | Negative |
P0757 | chr16:23641306 | Female | 69 | PALB2 | p.Met723fs | c.2167_2168delAT | Frameshift | Pathogenic | Negative | Negative |
P0732 | chr16:23646660 | Male | 56 | PALB2 | p.Leu403fs | c.1206delT | Frameshift | Pathogenic | Negative | Negative |
P0214 | chr17:7577545 | Male | 42 | TP53 | p.Met246Val | c.736A>G | Missense | Likely pathogenic | Negative | Negative |
P0493 | chr17:33428225 | Male | 68 | RAD51D | p.Arg320Ter | c.958C>T | Nonsense | Likely pathogenic | Negative | Father with pancreatic cancer |
P0774 | chr17:33430317 | Female | 80 | RAD51D | p.Arg252Ter | c.754C>T | Nonsense | Pathogenic | Colon polyps | Negative |
P1831 | chr17:33434458 | Male | 68 | RAD51D | p.Lys111fs | c.331_332insTA | Frameshift | Pathogenic | Negative | Negative |
P0417 | chr17:59857633 | Female | 75 | BRIP1 | p.Asn643fs | c.1923delT | Frameshift | Pathogenic | Negative | Negative |
P0437 | chr17:59858254 | Male | 59 | BRIP1 | p.Arg581Ter | c.1741C>T | Nonsense | Pathogenic | Negative | Negative |
P0581 | chr17:59858254 | Female | 69 | BRIP1 | p.Arg581Ter | c.1741C>T | Nonsense | Pathogenic | Negative | Negative |
P2568 | chr17:59878688 | Female | 60 | BRIP1 | p.Arg356Ter | c.1066C>T | Nonsense | Pathogenic | Negative | Negative |
P0519 | chr16:89833603 | Male | 57 | FANCA | p.Ser849fs | c.2546delC | Frameshift | Pathogenic | Negative | Negative |
P1545 | chr16:89866028 | Male | 49 | FANCA | p.Gln271Ter | c.811C>T | Nonsense | Pathogenic | Negative | Negative |
P0763 | chr9:98002929 | Male | 77 | FANCC | Splice | c.345 + 2GT>T | Noncoding | Likely pathogenic | Esophageal cancer | Negative |
P0437 | chr9:98002937 | Male | 59 | FANCC | p.Trp113Ter | c.339G>A | Nonsense | Likely pathogenic | Negative | Negative |
P1410 | chr7:152346380 | Male | 68 | XRCC2 | p.Arg64Ter | c.190C>T | Missense | Pathogenic | Negative | Negative |
P0201 | chr5:147207583 | Male | 51 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P0212 | chr5:147207583 | Male | 57 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P0322 | chr5:147207583 | Male | 68 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P0328 | chr5:147207583 | Male | 73 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P0357 | chr5:147207583 | Male | 54 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Chronic pancreatitis | Negative |
P0572 | chr5:147207583 | Male | 75 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P0727 | chr5:147207583 | Male | 77 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P0754 | chr5:147207583 | Male | 56 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P0907 | chr5:147207583 | Male | 70 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P1048 | chr5:147207583 | Male | 65 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P1435 | chr5:147207583 | Female | 41 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P1439 | chr5:147207583 | Male | 54 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P1501 | chr5:147207583 | Male | 65 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Father with gastric cancer |
P1513 | chr5:147207583 | Female | 57 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P1536 | chr5:147207583 | Female | 77 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P1555 | chr5:147207583 | Male | 72 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P1610 | chr5:147207583 | Male | 59 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P1732 | chr5:147207583 | Male | 61 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P2209 | chr5:147207583 | Male | 69 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P2519 | chr5:147207583 | Male | 78 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Negative | Negative |
P2556 | chr5:147207583 | Male | 64 | SPINK1 | Splice | c.194 + 2T>C | Noncoding | Pathogenic | Chronic pancreatitis | Father with lung cancer |
P1689 | chr7:117149143 | Female | 70 | CFTR | p.Arg74Trp | c.220C>T | Missense | Likely pathogenic | Negative | Negative |
P2293 | chr7:117149143 | Male | 49 | CFTR | p.Arg74Trp | c.220C>T | Missense | Likely pathogenic | Negative | Negative |
P1714 | chr7:117232086 | Male | 55 | CFTR | p.Gly622Asp | c.1865G>A | Missense | Pathogenic | Negative | Negative |
P1674 | chr7:117246728 | Male | 73 | CFTR | p.Gly970Asp | c.2909G>A | Missense | Likely pathogenic | Negative | Negative |
P1677 | chr7:117246728 | Male | 77 | CFTR | p.Gly970Asp | c.2909G>A | Missense | Likely pathogenic | Negative | Negative |
P2370 | chr7:117246728 | Male | 74 | CFTR | p.Gly970Asp | c.2909G>A | Missense | Likely pathogenic | Lymphosarcoma | Negative |
P0533 | chr7:117251704 | Male | 73 | CFTR | p.Arg1070Gln | c.3209G>A | Missense | Pathogenic | Negative | Negative |
P1681 | chr7:117254665 | Male | 66 | CFTR | Splice | c.3368-2A>G | Noncoding | Pathogenic | Negative | Negative |
Abbreviation: PDAC, pancreatic ductal adenocarcinomas.
Pathogenic classification according to the ClinVar database.15