Table 4.
Air-Bone Gaps by Group and Age Category
| Characteristic | > 10dBb | ≥ 20dBb | ≥ 30dBb |
|---|---|---|---|
|
| |||
| Overall | 44/102 (43.1%) | 22/102 (21.6%) | 3/102 (2.9%) |
| Genotype a | |||
| PEX1 – G843D/Null (1/9) | |||
| 0.5 kHz | 0/1 (0%) | ||
| 1.0 kHz | 0/1 (0%) | ||
| 2.0 kHz | 0/1 (0%) | ||
| 4.0 kHz | 0/1 (0%) | ||
| PEX1 – G843D/G843D (9/13) | |||
| 0.5 kHz | 23/52 (44.2%) | 10/52 (19.2%) | 2/52 (3.8%) |
| 1.0 kHz | 15/53 (28.3%) | 7/53 (13.2%) | 1/53 (1.9%) |
| 2.0 kHz | 3/36 (8.3%) | 1/36 (2.8%) | 1/36 (2.8%) |
| 4.0 kHz | 10/25 (40%) | 8/25 (32%) | 0/25 (0%) |
| Other PEX – Intermediate & Mild (6/17) | |||
| 0.5 kHz | 1/10 (10%) | 0/10 (0%) | |
| 1.0 kHz | 2/17 (11.8%) | 1/17 (5.9%) | 0/17 (0%) |
| 2.0 kHz | 3/13 (23.1%) | 2/13 (15.4%) | 0/13 (0%) |
| 4.0 kHz | 3/11 (27.3%) | 2/11 (18.2%) | 0/11 (0%) |
| DBPD (3/3) | |||
| 0.5 kHz | 4/19 (21.1%) | 0/19 (0%) | |
| 1.0 kHz | 1/20 (5%) | 0/20 (0%) | |
| 2.0 kHz | 0/20 (0%) | ||
| 4.0 kHz | 6/19 (31.6%) | 1/19 (5.3%) | 0/19 (0%) |
| Age Category | |||
| < 5 yrs. | 11/18 (61.1%) | 6/18 (33.3%) | 2/18 (11.1%) |
| 5 – 11 yrs. | 24/53 (45.3%) | 12/53 (22.6%) | 0/53 (0%) |
| 12 – 18 yrs. | 6/18 (33.3%) | 3/18 (16.7%) | 1/18 (5.6%) |
| > 18 yrs. | 3/13 (23.1%) | 1/13 (7.7%) | 0/13 (0%) |
a
Data indicates (number of patients) within each group with both AC and BC thresholds for air-bone gap calculations.
b
Data indicates number (percentage) of tests with air-bone gaps.