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. 2022 Feb 2;41(1):32-39. doi: 10.5937/jomb0-30420

Table 1. Hematologic differences between SCA and S/Beta in literature.

Patients & Tests HbSS Hb S/β0 Hb S/β+
RBC Morphology Normocytic Microcytic Microcytic
Normochromic Microchromic Microchromic
Hemoglobin Electrophoresis
A2 (%) <3.5 >3.5 >3.5
F (%) <10 <20 <20
A0 (%) 0 0 20–30
S (%) >90 >80 >60
Phenotype Usually Heavy Medium-Heavy Mild-Medium