Table 1.
Baseline data of the patients
| Baseline data | All patients (n = 28) | DSM (n = 17) | IDAVS (n = 3) | ADAVS (n = 8) |
|---|---|---|---|---|
| Males | 12 (42.9) | 10 (58.8) | 0 | 2 (25) |
| Age first symptoms (months) | 5 (0–167) | 4.5 (0–31) | 48 (2.5–167) | 26,5 (9–44) |
| Age diagnosis (months) | 14.5 (0–167) | 5 (0–31) | 48 (2.5–167) | 82 (12–127) |
| Age first consultation (months) | 19.5 (0–170) | 11 (0–72) | 54 (15–170) | 56.5 (13–114) |
| Presentation | ||||
| Antenatal | 2 (7.1) | 2 (11.8) | 0 | 0 |
| Seizure | 6 (21.4) | 4 (23.5) | 2 (66.7) | 0 |
| Hydrocephalus | 3 (10.7) | 3 (17.6) | 0 | 0 |
| Macrocrany | 11 (39.3) | 10 (58.8) | 1 (33.3) | 0 |
| Dilated facial veins | 9 (32.1) | 8 (47.1) | 0 | 1 (12.5) |
| Systemic repercussions (CHF, respiratory distress) | 4 (14.3) | 4 (23.5) | 0 | 0 |
| Developmental delay | 10 (35.7) | 9 (52.9) | 1 (33.3) | 0 |
| Intracranial hypertension | 2 (7.1) | 2 (11.8) | 0 | 0 |
| Focal neurologic deficit | 8 (28.6) | 6 (35.3) | 2 (66.7) | 0 |
| Exophtalmia | 3 (10.7) | 0 | 1 (33.3) | 2 (25) |
| Oculomotor palsy | 1 (3.6) | 1 (5.9) | 0 | 0 |
| Chemosis | 3 (10.7) | 1 (5.9) | 0 | 2 (25) |
| Bleeding | 2 (7.1) | 1 (5.9) | 1 (33.3) | 0 |
| Secondary bleeding | 2 (7.1) | 2 (11.8) | 0 | 0 |
| Incidental | 6 (21.4) | 0 | 0 | 6 (75) |
| Associated | ||||
| Facial lymphangioma | 3 (10.7) | 3 (17.6) | 0 | 0 |
| Facial AVM | 1 (3.6) | 0 | 1 (33.3) | 0 |
| Cardiac anomaly | 1 (3.6) | 1 (5.9) | 0 | 0 |
| Cavernoma | 2 (7.1) | 1 (5.9) | 1 (33.3) | 0 |
| DVA | 4 (14.3) | 3 (17.6) | 1 (33.3) | 0 |
| VGAM | 4 (14.3) | 0 | 0 | 4 (50) |
| Capillary malformations | 1 (3.6) | 1 (5.9) | 0 | 0 |
Data are presented as n(%). Mean ± SD or median (Q1–Q3).
DSM, dural sinus malformation; IDAVS, infantile dural arteriovenous shunt; ADAVS, adult-type dural arteriovenous shunt; CHF, congestive heart failure; AVM, arteriovenous malformation; DVA, developmental venous anomaly; VGAM, Vein of Galen aneurysmal malformation.