Table 2.
Proposed 3-Tier Staging of ROCM
| Stage 1: Sinonasal involvement | 1A: Involvement of 1 sinus and ipsilateral middle turbinate. |
| 1B: Involvement of >1 ipsilateral sinus and/or turbinate. | |
| 1C: Involvement of bilateral sinonasal cavities. | |
| Stage 2: Orbital involvement | 2A: Involvement of medial and/or inferior orbital compartment only. |
| 2B: Diffuse unilateral orbital involvement with or without optic nerve, nasolacrimal duct, and vascular involvement. | |
| 2C: Bilateral orbital involvement. | |
| Stage 3: Central nervous system involvement | 3A: Involvement of pachymeninges, cribriform plate, cavernous sinus/Meckel’s cave. |
| 3B: Vascular involvement (infarct/bleed)/perineural spread and skull base involvement. | |
| 3C: Leptomeningitis, cerebritis or abscess formation - focal or diffuse involvement. |
ROCM, rhino-orbital-cerebral mucormycosis.