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. Author manuscript; available in PMC: 2022 Mar 8.
Published in final edited form as: Clin Transplant. 2019 Oct 6;33(11):e13721. doi: 10.1111/ctr.13721

TABLE 3.

Literature review of domino liver transplantation (DLT) using maple syrup urine disease (MSUD) livers

Patient number MSUD donor age (y) DLT recipient age (y) DLT recipient diagnosis Follow-up period (mo) Outcome under protein-free diet
Khanna, et al14 1 25 51 HCV, Hepatocellular carcinoma 7 Normal leucine No disease symptom Normal graft function
Badell, et al37 1 24 52 Factor-8 deficiency, HIV, HCV 30
Feier, et al16 1
(received LDLT)		 2 2.75 BA 13
Mohan, et al17 2
(both received LDLT)		 1.8
3.2		 2
1.2		 LCH-sclerosing cholangitis BA 40–75
Matsunami, et al13 3
(all received LDLT)		 1
3.6
1.2		 1.9
2.3
2.8		 Protein C deficiency
BA
PHC		 8–16
Herden, et al20 14 (8 patients in detail, 1 patient loss with recurrent HCC) - 0.3–62.3 PSC, BA, HCC, unclear cirrhosis, urea cycle disorder, glycogen storage disease type-1 2–31